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2009 | OriginalPaper | Hoofdstuk

14 Metabole leverziekten

Auteurs : Prof.dr. H.J. Verkade, Dr. F.A.J.A. Bodewes, Dr. R. Houwen, Dr. R.A. de Vries, Dr. B. van Hoek, G. Visser

Gepubliceerd in: Leverziekten

Uitgeverij: Bohn Stafleu van Loghum

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Samenvatting

In dit hoofdstuk worden enkele metabole leverziekten behandeld. Alfa-1-antitrypsinedeficiëntie is een erfelijke aandoening die geassocieerd is met long- en leverziekte. Cystic fibrosis is geassocieerd met leverziekte, waaronder cirrose en portale hypertensie. De ziekte van Wilson, eveneens een erfelijke aandoening, is een stoornis in het kopermetabolisme met gevolgen voor de lever.
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Metagegevens
Titel
14 Metabole leverziekten
Auteurs
Prof.dr. H.J. Verkade
Dr. F.A.J.A. Bodewes
Dr. R. Houwen
Dr. R.A. de Vries
Dr. B. van Hoek
G. Visser
Copyright
2009
Uitgeverij
Bohn Stafleu van Loghum
DOI
https://doi.org/10.1007/978-90-313-7437-3_14