Skip to main content
Top
Gepubliceerd in: Netherlands Heart Journal 4/2024

Open Access 28-11-2023 | Heart Beat

ALCAPA syndrome, a rare cause of sudden cardiac death

Auteurs: Muniebur Rehman, Thijs Braber, Mohamed Mouden, Siert Knollema, Ahmet Güçlü

Gepubliceerd in: Netherlands Heart Journal | Uitgave 4/2024

share
DELEN

Deel dit onderdeel of sectie (kopieer de link)

  • Optie A:
    Klik op de rechtermuisknop op de link en selecteer de optie “linkadres kopiëren”
  • Optie B:
    Deel de link per e-mail
insite
ZOEKEN
Anomalous left coronary artery from the pulmonary artery (ALCAPA) syndrome is associated with a high mortality rate if untreated before the 1st year of life [1, 2]. Cardiac imaging remains of crucial importance in diagnosing and eventually treating this rare anomaly [15].
A previously healthy 41-year-old woman was presented to our emergency ward after an out-of-hospital cardiac arrest. Return of spontaneous circulation was achieved after defibrillation at 200 J. The electrocardiogram showed no signs of cardiac ischaemia. However, due to the initial rhythm being ventricular fibrillation and wall motion abnormalities on the emergency transthoracic echocardiogram, emergency coronary angiography was performed, revealing an aneurysmal right coronary artery and collaterals extending to the left coronary artery. Due to these anatomical peculiarities, coronary computed tomography angiography was performed, which showed the presence of ALCAPA (Fig. 1a, b). The patient was referred to a surgical centre, where she underwent treatment.

Conflict of interest

M. Rehman, T. Braber, M. Mouden, S. Knollema and A. Güçlü declare that they have no competing interests.
Open Access This article is licensed under a Creative Commons Attribution 4.0 International License, which permits use, sharing, adaptation, distribution and reproduction in any medium or format, as long as you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons licence, and indicate if changes were made. The images or other third party material in this article are included in the article’s Creative Commons licence, unless indicated otherwise in a credit line to the material. If material is not included in the article’s Creative Commons licence and your intended use is not permitted by statutory regulation or exceeds the permitted use, you will need to obtain permission directly from the copyright holder. To view a copy of this licence, visit http://​creativecommons.​org/​licenses/​by/​4.​0/​.
share
DELEN

Deel dit onderdeel of sectie (kopieer de link)

  • Optie A:
    Klik op de rechtermuisknop op de link en selecteer de optie “linkadres kopiëren”
  • Optie B:
    Deel de link per e-mail

Onze productaanbevelingen

Netherlands Heart Journal

Het Netherlands Heart Journal wordt uitgegeven in samenwerking met de Nederlandse Vereniging voor Cardiologie en de Nederlandse Hartstichting. Het tijdschrift is Engelstalig en wordt gratis beschikbaa ...

Literatuur
1.
go back to reference Cambronero-Cortinas E, Moratalla-Haro P, González-García AE, et al. Case report of asymptomatic very late presentation of ALCAPA syndrome: review of the literature since pathophysiology until treatment. Eur Heart J Case Rep. 2020;4:1–5.CrossRefPubMedPubMedCentral Cambronero-Cortinas E, Moratalla-Haro P, González-García AE, et al. Case report of asymptomatic very late presentation of ALCAPA syndrome: review of the literature since pathophysiology until treatment. Eur Heart J Case Rep. 2020;4:1–5.CrossRefPubMedPubMedCentral
2.
go back to reference Yau JM, Singh R, Halpern EJ, et al. Anomalous origin of the left coronary artery from the pulmonary artery in adults: a comprehensive review of 151 adult cases and a new diagnosis in a 53-year-old woman. Clin Cardiol. 2011;34:204–10.CrossRefPubMedPubMedCentral Yau JM, Singh R, Halpern EJ, et al. Anomalous origin of the left coronary artery from the pulmonary artery in adults: a comprehensive review of 151 adult cases and a new diagnosis in a 53-year-old woman. Clin Cardiol. 2011;34:204–10.CrossRefPubMedPubMedCentral
3.
go back to reference Baumgartner H, De Backer J, Babu-Narayan SV, et al. ESC guidelines for the management of adult congenital heart disease. Eur Heart J. 2020;2020:563–645. Baumgartner H, De Backer J, Babu-Narayan SV, et al. ESC guidelines for the management of adult congenital heart disease. Eur Heart J. 2020;2020:563–645.
5.
go back to reference Vilá Mollinedo LG, Uribe JA, Aceves Chimal JL, et al. Case report: ALCAPA syndrome: successful repair with an anatomical and physiological alternative surgical technique. F1000Res. 2016;5:1680.CrossRefPubMedPubMedCentral Vilá Mollinedo LG, Uribe JA, Aceves Chimal JL, et al. Case report: ALCAPA syndrome: successful repair with an anatomical and physiological alternative surgical technique. F1000Res. 2016;5:1680.CrossRefPubMedPubMedCentral
Metagegevens
Titel
ALCAPA syndrome, a rare cause of sudden cardiac death
Auteurs
Muniebur Rehman
Thijs Braber
Mohamed Mouden
Siert Knollema
Ahmet Güçlü
Publicatiedatum
28-11-2023
Uitgeverij
Bohn Stafleu van Loghum
Gepubliceerd in
Netherlands Heart Journal / Uitgave 4/2024
Print ISSN: 1568-5888
Elektronisch ISSN: 1876-6250
DOI
https://doi.org/10.1007/s12471-023-01829-5

Andere artikelen Uitgave 4/2024

Netherlands Heart Journal 4/2024 Naar de uitgave