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Gepubliceerd in: Netherlands Heart Journal 9/2023

Open Access 05-05-2023 | Rhythm Puzzle – Answer

A young man with DiGeorge syndrome and tachycardia

Auteurs: Nicolas Bradt, Leonie Franceus, Alice Fouckova, Becker Alzand

Gepubliceerd in: Netherlands Heart Journal | Uitgave 9/2023

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The 12-lead resting electrocardiogram (ECG) (Fig. 1) shows a broad QRS complex tachycardia, which is due to a supraventricular tachycardia with the pre-existing right bundle branch block. The underlying rhythm is a junctional ectopic tachycardia (JET). Further dissection of the rhythm shows an atrioventricular (AV) dissociation with a ventricular rhythm of 140 bpm and an atrial rhythm of around 95 bpm (Fig. 1, arrows). The slight irregularity in the rhythm is due to occasional capture/fusion beats (Fig. 1, asterisk).
The differentiation of a JET from other supraventricular tachycardias can be challenging, especially from atrioventricular nodal reentrant tachycardia when there is retrograde conduction to the atrium. Our patient has no retrograde conduction and for that reason no resetting of the sinus node with subsequent AV dissociation. This can be seen in Fig. 1 at the fourth and seventh QRS complex (marked with a hashtag). If there had been retrograde conduction these beats would have reset the tachycardia.
After the administration of adenosine (Fig. 2), the junctional rhythm is blocked while the sinus rhythm resumes but is slowed down. After the short period of normal sinus rhythm, the heart rate gradually increases and the junctional rhythm takes over again. This is referred to as a ‘warm-up pattern’, which typically occurs in a JET in contrast to other supraventricular tachycardias in which the heart rate suddenly increases.
Most cases of JET occur in children [1, 2]. A recent review showed that a JET is the most frequent supraventricular arrhythmia in the perioperative setting [2]. This case shows a JET in an older patient as a possible late complication of extensive cardiac surgery.
An electrophysiological study is needed for the confirmation of the diagnosis. However, our patient declined further examination.

Conflict of interest

N. Bradt, L. Franceus, A. Fouckova and B. Alzand declare that they have no competing interests.
Open Access This article is licensed under a Creative Commons Attribution 4.0 International License, which permits use, sharing, adaptation, distribution and reproduction in any medium or format, as long as you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons licence, and indicate if changes were made. The images or other third party material in this article are included in the article’s Creative Commons licence, unless indicated otherwise in a credit line to the material. If material is not included in the article’s Creative Commons licence and your intended use is not permitted by statutory regulation or exceeds the permitted use, you will need to obtain permission directly from the copyright holder. To view a copy of this licence, visit http://​creativecommons.​org/​licenses/​by/​4.​0/​.
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Netherlands Heart Journal

Het Netherlands Heart Journal wordt uitgegeven in samenwerking met de Nederlandse Vereniging voor Cardiologie en de Nederlandse Hartstichting. Het tijdschrift is Engelstalig en wordt gratis beschikbaa ...

Literatuur
1.
go back to reference Alasti M, Mirzaee S, Machado C, et al. Junctional ectopic tachycardia (JET). J Arrhythmia. 2020;36:837–44.CrossRef Alasti M, Mirzaee S, Machado C, et al. Junctional ectopic tachycardia (JET). J Arrhythmia. 2020;36:837–44.CrossRef
2.
go back to reference Cools E, Missant C. Junctional ectopic tachycardia after congenital heart surgery. Acta Anaesthesiol Belg. 2014;65:1–8.PubMed Cools E, Missant C. Junctional ectopic tachycardia after congenital heart surgery. Acta Anaesthesiol Belg. 2014;65:1–8.PubMed
Metagegevens
Titel
A young man with DiGeorge syndrome and tachycardia
Auteurs
Nicolas Bradt
Leonie Franceus
Alice Fouckova
Becker Alzand
Publicatiedatum
05-05-2023
Uitgeverij
Bohn Stafleu van Loghum
Gepubliceerd in
Netherlands Heart Journal / Uitgave 9/2023
Print ISSN: 1568-5888
Elektronisch ISSN: 1876-6250
DOI
https://doi.org/10.1007/s12471-023-01781-4

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