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Journal of Autism and Developmental Disorders

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18-08-2020 | Original Paper

Repetitive and Self-injurious Behaviors in Children with Cornelia de Lange Syndrome

Auteurs: Siddharth Srivastava, Bennett Clark, Colleen Landy-Schmitt, Elizabeth A. Offermann, Antonie D. Kline, Samuel T. Wilkinson, Marco A. Grados

Gepubliceerd in: Journal of Autism and Developmental Disorders | Uitgave 5/2021

Abstract

Cornelia de Lange syndrome (CdLS) is associated with repetitive and self-injurious behaviors (RBs, SIB). Evaluating children with CdLS, this study: (1) characterizes the spectrum of RBs; (2) characterizes the impact and severity of RBs including SIB; (3) describes how age and adaptive functioning relate to RBs including SIB. Fifty children (5–17 years) with CdLS were assessed with Children’s Yale-Brown Obsessive Compulsive Scale Modified for PDD; Aberrant Behavior Checklist (ABC); Vineland Adaptive Behaviors Scales (VABS). All children had ≥ 1 type of RB; 44% had some form of SIB. 64% spent > 1 h/day displaying RBs. Lower VABS adaptive functioning was associated with higher stereotypy and SIB scores (ABC). In children with CdLS, RBs including SIB are common, impactful, and associated with lower adaptive functioning.

vorige artikel I Have a Fear of Negative Evaluation, Get Me Out of Here! Examining Latent Constructs of Social Anxiety and Autistic Traits in Neurotypical and Autistic Young People

volgende artikel The Association Between Autism Spectrum Traits and the Successful Transition to Mainstream Secondary School in an Australian School-Based Sample

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Titel: Repetitive and Self-injurious Behaviors in Children with Cornelia de Lange Syndrome
Auteurs: Siddharth Srivastava
Bennett Clark
Colleen Landy-Schmitt
Elizabeth A. Offermann
Antonie D. Kline
Samuel T. Wilkinson
Marco A. Grados
Publicatiedatum: 18-08-2020
Uitgeverij: Springer US
Gepubliceerd in: Journal of Autism and Developmental Disorders / Uitgave 5/2021
Print ISSN: 0162-3257
Elektronisch ISSN: 1573-3432
DOI: https://doi.org/10.1007/s10803-020-04617-x

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