Abstract
The aim of our study was to provide a psychosocial and psychiatric evaluation of patients with epidermolysis bullosa (EB; a rare genetic disorder characterized by skin fragility), to assess psychological status, ascertain the presence of any psychiatric disorders and understand the impact of EB on quality of life. Twenty-five patients were assessed using a case record form and several standardized instruments. In 82% of patients, EB had a negative impact on quality of life and 80% of patients experienced psychiatric symptoms. Our findings revealed a high prevalence of psychosocial problems and psychiatric symptoms in patients with EB and suggested that a combined bio-psychosocial approach is the most appropriate therapeutic intervention.
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We gratefully acknowledge the support of the Pediatric Dermatology Association of Bari (http://www.dermatologiapediatrica.com).
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Margari, F., Lecce, P.A., Santamato, W. et al. Psychiatric Symptoms and Quality of Life in Patients Affected by Epidermolysis Bullosa. J Clin Psychol Med Settings 17, 333–339 (2010). https://doi.org/10.1007/s10880-010-9205-4
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DOI: https://doi.org/10.1007/s10880-010-9205-4