Abstract
In the humanities and in the social sciences, it is almost a truism to say that one cannot escape the influence of one’s own historical time. Certain novelists of the past, for example, are highly valued during one historical period, “lost” to another, only to be reembraced at a later time. Similarly in a field like history, we see changes over the decades in how society views the accomplishments of certain individuals. Are Jefferson, Adams, Franklin, and other of America’s “Founding Fathers” omniscient visionaries, as portrayed in many recent books, or instead should they be criticized for leaving unresolved such basic national issues as slavery (Brands, 2003)? Fields, like people, reflect the times in which they exist.
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REFERENCES
Abbeduto, L., & Keller-Bell, Y. (2002). Review of genetics and mental retardation syndromes: A new look at behavior and interventions. American Journal on Mental Retardation, 107, 412–414.
Aman, M. G., & Singh, N. N. (1994). Aberrant Behavior Checklist—community supplementary manual. East Aurora, NY: Slosson Educational.
Anderson, L., & Ernst, M. (1994). Self-injury in Lesch–Nyhan disease. Journal of Autism and Developmental Disorders, 24, 67–81.
Barnard, L., Pearson, J., Rippon, L., & O’Brien, G. (2002). Behavioural phenotypes of genetic syndromes: Summaries, including notes on management and therapy. In G. O’Brien (Ed.), Behavioural phenotypes in clinical practice (pp. 169–227). London, England: Mac Keith.
Baumgardner, T. L., Reiss, A. L., Freund, L. S., & Abrams, M. T. (1995). Specification of the neurobehavioral phenotype in males with fragile X syndrome. Pediatrics, 95, 744–752.
Bell, R. Q. (1968). A reinterpretation of direction of effects in studies of socialization. Psychological Review, 75, 81–95.
Brands, H. W. (2003). Founders chic. The Atlantic, 292(2), 101–110.
Bregman, J. D., Leckman, J. F., & Ort, S. I. (1988). Fragile X syndrome: Genetic predisposition onto psychopathology. Journal of Autism and Developmental Disorders, 18, 343–354.
Butler, M. G., Bittel, D. C., Kibiryeva, N., Talebizadeh, Z., & Thompson, T. (2004). Behavioral differences among subjects with Prader–Willi syndrome and type I or type II deletion and maternal disomy. Pediatrics, 113, 565–573.
Cahill, B. M., & Glidden, L. M. (1996). Influence of child diagnosis on family and parent functioning: Down syndrome versus other disabilities. American Journal on Mental Retardation, 101, 149–160.
Carlin, M. E. (1990). The improved prognosis in cri du chat (5p-) syndrome. In W. I. Fraser (Ed.), Proceedings of the 8th Congress of the International Association of the Scientific Study of Mental Deficiency (pp. 64–73). Edinburgh, UK: Blackwell.
Carr, J. (1995). Down’s syndrome: Children growing up. Cambridge, UK: Cambridge University Press.
Chapman, R. S., & Hesketh, L. J. (2000). Behavioral phenotype of individuals with Down syndrome. Mental Retardation and Developmental Disabilities Research Reviews, 6, 84–95.
Collacott, R. A. (1992). The effect of age and residential placement on adaptive behavior of adults with Down’s syndrome. British Journal of Psychiatry, 161, 675–679.
Conners, F. A., Rosenquist, C. J., Atwell, J. A., & Klinger, L. G. (2000). Cognitive strengths and weaknesses associated with Prader–Willi syndrome. Education and Training in Mental Retardation and Developmental Disabilities, 35, 441–448.
Cornish, K. M., & Pigram, J. (1996). Developmental and behavioural characteristics of cri du chat syndrome. Archives of Diseases in Childhood, 75, 448–450.
Crowe, S., & Hay, D. (1990). Neuropsychological dimensions of the fragile X syndrome: Support for a non-dominant hemisphere dysfunction hypothesis. Neuropsychologia, 28, 9–16.
Dimitropoulos, A., Feurer, I. D., Butler, M. G., & Thompson, T. (2001). Emergence of compulsive behavior and tantrums in children with Prader–Willi syndrome. American Journal on Mental Retardation, 106, 39–51.
Dimitropoulos, A., Feurer, I. D., Roof, E., Stone, W., Butler, M. G., Sutcliffer, J., et al. (2000). Appetitive behavior, compulsivity, and neurochemistry in Prader–Willi syndrome. Mental Retardation and Developmental Disabilities Research Reviews, 6, 125–130.
Don, A. J., Schellenberg, E. G., & Rourke, B. P. (1999). Music and language skills of children with Williams syndrome. Child Neuropsychology, 5, 154–170.
Dorn, B., & Goff, B. J. (2003). The student with Prader–Willi syndrome: Information for educators. Sarasota, FL: Prader–Willi Syndrome Association (USA); Retrieved July 17, 2006 from www.pwsausa.org
Dykens, E. M. (1995). Measuring behavioral phenotypes: Provocations from the “new genetics.” American Journal on Mental Retardation, 99, 522–532.
Dykens, E. M. (1999). Prader–Willi syndrome. In H. Tager-Flusberg (Ed.), Neurodevelopmental disorders (pp. 137–154). Cambridge, MA: MIT Press.
Dykens, E. M. (2000). Psychopathology in children with intellectual disability. Journal of Child Psychology and Psychiatry, 41, 407–417.
Dykens, E. M. (2002). Are jigsaw puzzle skills “spared” in persons with Prader–Willi syndrome? Journal of Child Psychology and Psychiatry, 43, 343–352.
Dykens, E. M. (2003). Anxiety, fears, and phobias in persons with Williams syndrome. Developmental Neuropsychology, 23, 291–316.
Dykens, E. M. (2004). Maladaptive behaviors and compulsions in Prader–Willi syndrome: New insights from older adults. American Journal on Mental Retardation, 109, 142–153.
Dykens, E. M., Cassidy, S. B., & King, B. H. (1999). Maladaptive behavior differences in Prader–Willi syndrome due to paternal deletion versus maternal uniparental disomy. American Journal on Mental Retardation, 104, 67–77.
Dykens, E. M., & Clarke, D. J. (1997). Correlates of maladaptive behavior in individuals with 5p- (cri du chat) syndrome. Developmental Medicine and Child Neurology, 39, 752–756.
Dykens, E. M., Finucane, B. M., & Gayley, C. (1997). Brief report: Cognitive and behavioral profiles in persons with Smith–Magenis syndrome. Journal of Autism and Developmental Disorders, 27, 203–211.
Dykens, E. M., & Hodapp, R. M. (1997). Treatment issues in genetic mental retardation syndromes. Professional Psychology: Research and Practice, 28, 263–270.
Dykens, E. M., & Hodapp, R. M. (2001). Research in mental retardation: Toward an etiologic approach. Journal of Child Psychology and Psychiatry, 42, 49–71.
Dykens, E. M., Hodapp, R. M., & Leckman, J. F. (1987). Strengths and weaknesses in intellectual functioning of males with fragile X syndrome. American Journal of Mental Deficiency, 92, 234–236.
Dykens, E. M., Hodapp, R. M., Walsh, K. K., & Nash, L. (1992). Profiles, correlates, and trajectories of intelligence in Prader–Willi syndrome. Journal of the American Academy of Child and Adolescent Psychiatry, 31, 1125–1130.
Dykens, E. M., & Kasari, C. (1997). Maladaptive behavior in children with Prader–Willi syndrome, Down syndrome, and non-specific mental retardation. American Journal on Mental Retardation, 102, 228–237.
Dykens, E. M., Leckman, J. F., & Cassidy, S. B. (1996). Obsessions and compulsions in Prader–Willi syndrome. Journal of Child Psychology and Psychiatry, 37, 995–1002.
Dykens, E. M., & Rosner, B. A. (1999). Refining behavioral phenotypes: Personality-motivation in Williams and Prader–Willi syndromes. American Journal on Mental Retardation, 104, 158–169.
Dykens, E. M., Hodapp, R. M., & Finucane, B. M. (2000). Genetics and mental retardation syndromes: A new look at behavior and genetics. Baltimore, MD: Paul H. Brookes Publishing Company.
Dykens, E. M., & Shah, B. (2003). Psychiatric disorders in Prader–Willi syndrome: Epidemiology and treatment. CNS Drugs, 17, 167–178.
Dykens, E. M., Shah, B., Sagun, J., Beck, T., & King, B. Y. (2002). Maladaptive behaviour in children and adolescents with Down’s syndrome. Journal of Intellectual Disability Research, 46, 484–492.
Dykens, E. M., & Smith, A. C. M. (1998). Distinctiveness and correlates of maladaptive behaviour in children and adolescents with Smith–Magenis syndrome. Journal of Intellectual Disability Research, 42, 481–489.
Einfeld, S. L. (2004). Behaviour phenotypes of genetic disorders. Current Opinion in Psychiatry, 17, 343–349.
Einfeld, S. L., & Tonge, B. J. (1992). Manual for the Developmental Behaviour Checklist: Primary carer version. Australia: School of Psychiatry, University of New South Wales.
Ellis, N. R. (1969). A behavioral research strategy in mental retardation: Defense and critique. American Journal on Mental Deficiency, 73, 557–566.
Fidler, D. J., Hodapp, R. M., & Dykens, E. M. (2000). Stress in families of young children with Down syndrome,Williams syndrome, and Smith–Magenis syndrome. Early Education and Development, 11, 395–406.
Finucane, B., Dirrigl, K. H., & Simon, E. W. (2001). Characterization of self-injurious behaviors in children and adults with Smith–Magenis syndrome. American Journal on Mental Retardation, 106, 52–58.
Finucane, B. M. (1996). What’s so special about genetics? A guide for special educators. Elwyn, PA: Elwyn.
Finucane, B. M., Konar, D., Haas-Givler, B., Kurtz, M. D., & Scott, L. I. (1994). The spasmodic upper-body squeeze: A characteristic behavior in Smith–Magenis syndrome. Developmental Medicine and Child Neurology, 36, 78–83.
Flint, J., & Yule, W. (1994). Behavioural phenotypes. In M. Rutter, E. Taylor, & L. Hersov (Eds.), Child and adolescent psychiatry: Modern approaches (3rd ed., pp. 666–687). London: Blackwell Scientific.
Fowler, A. E. (1990). Language abilities in children with Down Syndrome: Evidence for a specific syntactic delay. In D. Cicchetti & M. Beeghly (Eds.), Children with Down syndrome: A developmental approach (pp. 302–328). New York: Cambridge University Press.
Gersh, M., Goodart, S. A., Pasztor, L. M., Harris, D. J., Weiss, L., & Overhauser, J. (1995). Evidence for a distinct region causing a cat-like cry in patients with 5p- deletions. American Journal of Human Genetics, 56, 1404–1410.
Gosch, A., & Pankau, R. (1994). Social–emotional and behavioral adjustment in children with Williams syndrome. American Journal of Medical Genetics, 53, 335–339.
Greenberg, F., Lewis, R. A., Potocki, L., Glaze, D., Parke, J., Killian, J. (1996). Multidisciplinary clinical study of Smith–Magenis syndrome: Deletion 17p11.2. American Journal of Medical Genetics, 62, 247–254.
Hagerman, R. J. (1996). Fragile X syndrome. Child and Adolescent Psychiatric Clinics of North America, 5, 895–911.
Hagerman, R. J. (1999). Psychopharmacological interventions in fragile X syndrome, fetal alcohol syndrome, Prader–Willi syndrome, Angelman syndrome, Smith–Magenis syndrome, and velocardiofacial syndrome. Mental Retardation and Developmental Disabilities Research Reviews, 5, 305–313.
Hodapp, R. M. (1997). Direct and indirect behavioral effects of different genetic disorders of mental retardation. American Journal on Mental Retardation, 102, 67–79.
Hodapp, R. M. (1999). Indirect effects of genetic mental retardation disorders: Theoretical and methodological issues. International Review of Research in Mental Retardation, 22, 27–50.
Hodapp, R. M., & Dykens, E. M. (1994). Mental retardation’s two cultures of behavioral research. American Journal on Mental Retardation, 98, 675–687.
Hodapp, R. M., & Dykens, E. M. (2001). Strengthening behavioral research on genetic mental retardation disorders. American Journal on Mental Retardation, 106, 4–15.
Hodapp, R. M., & Dykens, E. M. (2004). Studying behavioral phenotypes: Issues, benefits, challenges. In E. Emerson, C. Hatton, T. Parmenter, & T. Thompson (Eds.), International handbook of applied research in intellectual disabilities (pp. 203–220). New York: Wiley.
Hodapp, R. M., Dykens, E. M., Ort, S. I., Zelinsky, D. G., & Leckman, J. F. (1991). Changing patterns of intellectual strengths and weaknesses in males with fragile X syndrome. Journal of Autism and Developmental Disorders, 21, 503–516.
Hodapp, R. M., Evans, D. W., & Gray, F. L. (1999). Intellectual development in children with Down syndrome. In J. Rondal, J. Perera, & L. Nadel (Eds.), Down syndrome: A review of current knowledge (pp. 124–132). London: Whurr.
Hodapp, R. M., & Fidler, D. J. (1999). Special education and genetics: Connections for the 21st century. The Journal of Special Education, 33, 130–137.
Hodapp, R. M., Ly, T. M., Fidler, D. J., & Ricci, L. A. (2001). Less stress, more rewarding: Parenting children with Down syndrome. Parenting: Science and Practice, 1, 317–337.
Hodapp, R. M., Ricci, L. A., Ly, T. M., & Fidler, D. J. (2003). The effects of the child with Down syndrome on maternal stress. British Journal of Developmental Psychology, 22, 137–151.
Hornby, G. (1995). Fathers’ views of the effects on their families of children with Down syndrome. Journal of Child and Family Studies, 4, 103–117.
Jarrold, C., Baddeley, A. D., & Hewes, A. K. (2000). Verbal short-term memory deficits in Down syndrome: A consequence of problems in rehearsal? Journal of Child Psychology and Psychiatry and Allied Disciplines, 41, 223–244.
Jarrold, C., Baddeley, A. D., Hewes, A. K., & Phillips, C. (2001). A longitudinal assessment of diverging verbal and non-verbal abilities in the Williams syndrome phenotype. Cortex, 37, 423–431.
Jarrold, C., Baddeley, A. D., & Phillips, C. E. (2002). Verbal short-term memory in Down syndrome: A problem of memory, audition, or speech? Journal of Speech, Language, and Hearing Research, 45, 531–544.
Jarrold, C., Hartley, S. J., Phillips, C., & Baddeley, A. D. (2000). Word fluency in Williams syndrome: Evidence for unusual semantic organization? Cognitive Neuropsychiatry, 5, 292–319.
Kasari, C., & Sigman, M. (1997). Linking parental perceptions to interactions in young children with autism. Journal of Autism and Developmental Disorders, 27, 39–57.
Kaufman, A. S., & Kaufman, N. L. (1983). Kaufman Assessment Battery for children. Circle Pines, MN: American Guidance Service.
Kemper, M. B., Hagerman, R. J., & Altshul-Stark, D. (1988). Cognitive profiles of boys with fragile X syndrome. American Journal of Medical Genetics, 30, 191–200.
Klein, B. P., & Mervis, C. B. (1999). Contrasting patterns of cognitive abilities of 9- and 10- year-olds with Williams syndrome or Down syndrome. Developmental Neuropsychology, 16, 177–196.
Kumin, L. (1994). Intelligibility of speech in children with Down syndrome in natural settings: Parents’ perspective. Perceptual and Motor Skills, 78, 307–313.
Levine, K. (1994). Williams syndrome: Information for teachers. Clawson, MI: The Williams Syndrome Association.
Levine, K., & Wharton, R. H. (1993). Children with Prader–Willi syndrome: Information for school staff. Roslyn Heights, NY: Visible Ink (available through the Prader–Willi Syndrome Association, US; Retrieved July 17, 2006 from www.pwsausa.org).
Meyers, B. A., & Pueschel, S. M. (1991). Psychiatric disorders in persons with Down syndrome. Journal of Nervous and Mental Disease, 179, 609–613.
Miller, J. F. (1999). Profiles of language development in children with Down syndrome. In J. F. Miller, M. Leddy, & L. A. Leavitt (Eds.), Improving the communication of people with Down syndrome (pp. 11–39). Baltimore, MD: Paul H. Brookes.
Mount, R. H., Charman, T., Hastings, R. P., Reilly, S., & Cass, H. (2002). The Rett Syndrome Behavior Questionnaire (RSBQ): Refining the behavioral phenotype of Rett syndrome. Journal of Child Psychology and Psychiatry, 43, 1099–1110.
Mount, R. H., Charman, T., Hastings, R. P., Reilly, S., & Cass, H. (2003). Features of autism in Rett syndrome and severe mental retardation. Journal of Autism and Developmental Disorders, 33, 435–442.
Naglieri, J. A. (1985). Assessment of mentally retarded children with the Kaufman Assessment Battery for Children. American Journal of Mental Deficiency, 89, 367–371.
O’Brien, G. (2002a). The clinical practice of behavioural phenotypes. In G. O’Brien (Ed.), Behavioural phenotypes in clinical practice (pp. 1–12). London, England: Mac Keith.
O’Brien, G. (Ed.). (2002b). Behavioural phenotypes in clinical practice. London, England: Mac Keith.
Obrzut, A., Nelson, R. B., & Obrzut, J. E. (1987). Construct validity of the Kaufman Assessment Battery for Children with mildly mentally retarded students. American Journal of Mental Deficiency, 92, 74–77.
Opitz, J. M. (1985). Editorial comment: The developmental field concept. American Journal of Medical Genetics, 21, 1–11.
Papolos, D. F., Faedda, G. L., Veit, S., Goldberg, R., Morrow, B., et al. (1996). Bipolar spectrum disorders in patients diagnosed with velo-cardio-facial syndrome: Does a hemizygous deletion on chromosome 22q11 result in bipolar affective disorder? American Journal of Psychiatry, 153, 1541–1547.
Pennington, B. F., Moon, J., Edgin, J., Stedron, J., & Nadel, L. (2003). The neuropsychology of DS: Evidence for hippocampal dysfunction. Child Development, 74, 75–93.
Pennington, B. F., O’Connor, B., & Sudhalter, V. (1991). Toward a neuropsychology of fragile X syndrome. In R. J. Hagerman & A. C. Silverman (Eds.), Fragile X syndrome: Diagnosis, treatment, and research (pp. 173–201). Baltimore, MD: The Johns Hopkins.
Pezzini, G., Vicari, S., Volterra, V., Milani, L., & Osella, M. T (1999). Children with Williams syndrome: Is there a single neuropsychological profile? Developmental Neuropsychology, 15, 141–155.
Pulver, A. E., Nestadt, G., Shpritzen, R. J., Lamacz, M., Wolyniec, P. S., Morrow, B., et al. (1994). Psychotic illness in patients diagnosed with velo-cardio-facial syndrome and their relatives. Journal of Nervous and Mental Disease, 182, 476–478.
Reiss, S. (1988). The Reiss screen for maladaptive behavior. Worthington, OH: IDS.
Rogers, S. J., Wehner, E. A., & Hagerman, R. (2001). The behavioral phenotype of fragile X: Symptoms of autism in very young children with fragile X syndrome, idiopathic autism, and other developmental disorders. Journal of Developmental and Behavioral Pediatrics, 22, 409–417.
Rondal, J. (1995). Exceptional language development in Down syndrome. New York: Cambridge University Press.
Roof, E., Stone,W., MacLean,W., Feurer, I. D., Thompson, T., et al. (2000). Intellectual characteristics of Prader–Willi syndrome: Comparison of genetic subtypes. Journal of Intellectual Disability Research, 44, 25–30.
Rosner, B. A., Hodapp, R. M., Fidler, D. J., Sagun, J. N., & Dykens, E. M. (2004). Social competence in persons with Prader–Willi, Williams, and Down syndromes. Journal of Applied Research in Intellectual Disabilities, 17, 209–217.
Thomas, V., & Olsen, D. H. (1993). Problem families and the circumplex model: Observational assessment using the clinical rating scale (CRS). Journal of Marital and Family Therapy, 19, 159–175.
Tonge, B. J., & Einfeld, S. L. (2003). Psychopathology and intellectual disability: The Australian child to adult longitudinal study. International Review of Research in Mental Retardation, 26, 61–91.
Udwin, O. (1990). A survey of adults with Williams syndrome and idiopathic infantile hypercalcaemia. Developmental Medicine and Child Neurology, 32, 129–141.
Udwin, O., & Yule, W. (2001). Guidelines for teachers. [On-line]. Retrieved July 17, 2006 from: www.wsf.org
Udwin, O., Yule, W., & Martin, N. (1987). Cognitive abilities and behavioural characteristics of children with idiopathic infantile hypercalcaemia. Journal of Child Psychology and Psychiatry and Allied Disciplines, 28, 297–309.
Van Acker, R. (1991). Rett syndrome: A review of current knowledge. Journal of Autism and Developmental Disorders, 21, 381–406.
Vogels, A., De Hert, M., Descheemaeker, M. J., Govers, V., Devriendt, K., Legius, E., et al. (2004). Psychotic disorders in Prader–Willi syndrome. American Journal of Medical Genetics, 127A(Pt. A), 238–243.
Wigren, M., & Heimann, M. (2001). Excessive picking in Prader–Willi syndrome: A pilot study of phenomenological aspects and comorbid symptoms. International Journal of Disability, Development and Education, 48, 129–142.
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Hodapp, R.M., Dykens, E.M. (2007). Behavioral Effects of Genetic Mental Retardation Disorders. In: Jacobson, J.W., Mulick, J.A., Rojahn, J. (eds) Handbook of Intellectual and Developmental Disabilities. Issues on Clinical Child Psychology. Springer, Boston, MA. https://doi.org/10.1007/0-387-32931-5_6
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