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(Komplexe) Angeborene Herzfehler mit überwiegendem Rechts-Links-Shunt

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Pädiatrische Kardiologie

Zusammenfassung

Die Fallot-Tetralogie wurde erstmals im Jahre 1571 von Nils Stensen und danach 1777 von Sandifort, 1784 von Hunter und 1866 von Peacock pathologisch-anatomisch beschrieben [8]. Fallot wies 1888 auf die vier anatomischen Befunde hin, die der Tetralogie zugrunde liegen [11].

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Literatur

  1. Apitz J (1980) Indikationen zur Reoperation bei kongenitalen Angiokardiopathien. Therapiewoche 30: 2328–2339

    Google Scholar 

  2. Apitz J, Beuren AI (1963) Angeborene Herzfehler im ersten Lebensjahr. Arch Kreisl Forsch 42: 264–276

    Article  CAS  Google Scholar 

  3. Apitz J, Stoermer J (1967) Über die Lebensaussichten von Säuglingen mit kongenitalen Angiokardiopathien. Mschr Kinderheilk 115: 95–102

    PubMed  CAS  Google Scholar 

  4. Apitz J, Frey R, Bleicher W, Epple E, Schmaltz AA, Steil E, Kemter BE (1981) Intensivüberwachung in der Pädiatrie mit Hilfe eines Rechnersystems. Mschr Kinderheilk 129: 105 —109

    Google Scholar 

  5. Apitz J, Sieverding L, Breuer J, Baden W, Steil E (1995) Der Stellenwert der invasiven kardiologischen Diagnostik. Mschr Kinderheilk 143: 475–480

    Google Scholar 

  6. Becker AE, Anderson RH (1981) Pathology of congenital heart disease. Butterworths, London, pp 191–198

    Google Scholar 

  7. Becker AE, Anderson RH (1985) Pathologie des Herzens. Thieme, Stuttgart, S 198–202

    Google Scholar 

  8. Beuren AJ (1964) Die Fallot’sche Tetralogie und Trilogie, Pathologie, Pathophysiologie und Klinik. Erg Inn Med u Kinderheilkd. Springer, Berlin Göttingen Heidelberg, Bd 21: S1–47

    Google Scholar 

  9. Castaneda AR, Jonas RA, Mayer JE, Hanley FL (1994) Cardiac surgery of the neonate and infant. WB Saunders, Philadelphia, pp 215–234

    Google Scholar 

  10. Edwards JE (1960) Congenital malformations of the heart and great vessels. In: Gould SE (ed) Pathology of the heart, 2“d ed. Ch C Thomas Publ., Springfield Ill., USA, pp 317–335

    Google Scholar 

  11. Fallot E (1888) Contribution à l’anatomie pathologique de la maladie bleu (cianose cardiaque). Marseille — méd 25:77, 138, 207, 270, 341, 403

    Google Scholar 

  12. Fyler DC (1992) Nadas ‘Pediatric Cardiology. Hanley und Belfus, Philadelphia, pp 471–491

    Google Scholar 

  13. Gussenhoven EJ, Becker AE (1983) Congenital heart disease. Churchill Livingstone, New York, pp 131–136

    Google Scholar 

  14. Henes W, Beyer A, Steil E, Hassberg D (1992) Spiroergometrische Untersuchungen nach Korrekturoperation einer Fallot’schen Tetralogie. Klin Pädiatr 204: 428–433

    Article  PubMed  CAS  Google Scholar 

  15. Hofbeck M (1994) Fallot’sche Tetralogie und Pulmonalatresie. In: Schmaltz AA, Singer H (Hrsg) Herzoperierte Kinder und Jugendliche. Wiss Verlagsges, Stuttgart, S 151–160

    Google Scholar 

  16. Johnson AM (1961) Norepinephrine and cyanotic attacks in Fallot’s tetralogy. Brit Heart J 23: 197–202

    Article  PubMed  CAS  Google Scholar 

  17. Keith JD, Rowe RD, Vlad P (1979) Heart Disease in infancy and childhood, 3rd ed. Macmillan Comp, New York, pp 470–505

    Google Scholar 

  18. Kirklin JW, Barratt-Boyes BG (1986) Cardiac Surgery. Wiley, New York, pp 699–819

    Google Scholar 

  19. Lillehei CW, Cohen M, Warden HE, Read RC, Aust JB, DeWall RA, Varco RL (1955) Direct vision intracardiac surgical correction of the tetralogy of Fallot, pentalogy of Fallot and pulmonary atresia defects. Ann Surg 142: 418–443

    Article  PubMed  CAS  Google Scholar 

  20. Neches WH, Park SC, Ettedgui JA (1990) Tetralogy of Fallot and Tetralogy of Fallot with pulmonary atresia. In: Garsson A, Bricker JT, McNamara DG (eds) The science and practice of Pediatric Cardiology, Lea und Febiger, Philadelphia, pp 1073–1100

    Google Scholar 

  21. Schmaltz AA, Leitritz H, Apitz J, Kemter BE, Löser H, Tjhen KY (1977) Propranolol bei der Fallot’schen Tetralogie: Hämodynamische Unterschungen und ihre klinische Anwendung. Mschr Kinderheilk 125: 195–201

    Google Scholar 

  22. Sieverding L, Klose U, Apitz J (1990) Morphological diagnosis of congenital and acquired heart disease by Magnetic Resonance Imaging. Pediatr Radiol 20: 311–319

    Article  PubMed  CAS  Google Scholar 

  23. Taussig HB (1960) Congenital malformations of the heart, 2“d ed. Commonwealth Fund, Cambridge, USA, pp 3–61

    Google Scholar 

  24. Weller R, Steil E, Bleicher W, Apitz J (1979) Ein Beitrag zum Kreislaufverhalten bei zyanotischen Herzvitien mit Lungendurchblutung über einen PDA. Therapiewoche 29: 4836–4840

    Google Scholar 

  25. Alfieri O, Blackstone EH, Kirklin JW, Pacifico AD, Bargeron LMJ (1978) Surgical treatment of tetralogy of Fallot with pulmonary atresia. J Thorac Cardiovasc Surg 76: 321–335

    PubMed  CAS  Google Scholar 

  26. Alfieri O, Blackstone EH, Parenzan L (1979) Growth of the pulmnary anulus and pulmonary arteries after the Waterston anastomosis. J Thorac Cardiovasc Surg 78: 440–444

    PubMed  CAS  Google Scholar 

  27. Barbero Marcial M, Rizzo A, Lopes AA, Bittencourt D, Junior JO, Jatene AD (1987) Correction of pulmonary atresia with ventricular septal defect in the absence of the pulmonary trunk and the central pulmonary arteries (so-called truncus type IV). J Thorac Cardiovasc Surg 94: 911–914

    PubMed  CAS  Google Scholar 

  28. Blackstone EH, Shimazaki Y, Maehara T, Kirklin JW, Bargeron LMJ (1988) Prediction of severe obstruction to right ventricular outflow after repair of tetralogy of Fallot and pulmonary atresia. J Thorac Cardiovasc Surg 96: 288–293

    PubMed  CAS  Google Scholar 

  29. Bogers AJ, Rohmer J, Wolsky SA, Quaegebeur JM, Huysmans HA (1990) Coronary artery fistula as source of pulmonary circulation in pulmonary atresia with ventricular septal defect. Thorac Cardiovasc Surg 38: 30–32

    Article  PubMed  CAS  Google Scholar 

  30. Bull K, Somerville J, Ty E, Spiegelhalter D (1995) Presentation and attrition in complex pulmonary atresia. J Am Coll Cardiol 25: 491–499

    Article  PubMed  CAS  Google Scholar 

  31. Castaneda AR, Mayer JE, Lock JE (1992) Tetralogy of Fallot, pulmonary atresia, and diminutive pulmonary arteries. Prog Pediatr Cardiol 1: 50–60

    Article  Google Scholar 

  32. Di Donato RM, Jonas RA, Lang P, Rome JJ, Mayer JEJ, Castaneda AR (1991) Neonatal repair of tetralogy of Fallot with and without pulmonary atresia. J Thorac Cardiovasc Surg 101: 126–137

    PubMed  Google Scholar 

  33. Dodelin C, Sidi D, Piechaud JF, Iserin L, Bonnet D, Aggoun Y, Kachaner J (1995) Pulmonary atresia with ventricular septal defect: therapeutic strategy in newborn infants. Arch Mal Coeur Vaiss 88: 681–686

    PubMed  CAS  Google Scholar 

  34. Freedom RM, Pongiglione G, Williams WG, Trusler GA, Moes CA, Rowe RD (1983) Pulmonary vein wedge angiography: indications, results, and surgical correlates in 25 patients. Am J Cardiol 51: 936–941

    Article  PubMed  CAS  Google Scholar 

  35. Freedom RM, Pongiglione G, Williams WG, Truster GA, Rowe RD (1983) Palliative right ventricular outflow tract construction for patients with pulmonary atresia, ventricular septal defect, and hypoplastic pulmonary arteries. J Thorac Cardiovasc Surg 86: 24–36

    PubMed  CAS  Google Scholar 

  36. Gale AW, Arciniegas E, Green EW, Blackstone EH, Kirklin JW (1979) Growth of the pulmonary anulus and pulmonary arteries after the Blalock-Taussig shunt. J Thorac Cardiovasc Surg 77: 459–465

    PubMed  CAS  Google Scholar 

  37. Gibbs JL, Rothman MT, Rees MR, Parsons JM, Blackburn ME, Ruiz CE (1992) Stenting of the arterial duct: a new approach to palliation for pulmonary atresia. Br Heart J 67: 240–245

    Article  PubMed  CAS  Google Scholar 

  38. Hadjo A, Jiminez M, Baudet E, Roques X, Laborde N, Srour S, Surrel C, Choussat A (1995) Review of the long-term cours of 52 patients with pulmonary atresia and ventricular septal defect. Anatomical and surgical considerations. Eur H J 16: 1668–1674

    Google Scholar 

  39. Haroutunian LM, Neill CA (1972) Pulmonary complications of congenital heart disease: hemoptysis. Am Heart J 84: 540–559

    Article  PubMed  CAS  Google Scholar 

  40. Haworth SG (1980) Collateral arteries in pulmonary atresia with ventricular septal defect. A precarious blood supply. Br Heart J 44: 5–13

    Article  PubMed  CAS  Google Scholar 

  41. Haworth SG, Macartney FJ (1980) Growth and development of pulmonary circulation in pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries. Br Heart J 44: 14–24

    Article  PubMed  CAS  Google Scholar 

  42. Haworth SG, Reid L (1977) Quantitative structural study of pulmonary circulation in the newborn with pulmonary atresia. Thorax 32: 129–133

    Article  PubMed  CAS  Google Scholar 

  43. Hofheck M, Sunnegardh JT, Burrows PE, Moes CA, Lightfoot N, Williams WG, Trusler GA, Freedom RM (1991) Analysis of survival in patients with pulmonic valve atresia and ventricular septal defect. Am J Cardiol 67: 737–743

    Article  Google Scholar 

  44. Hruda J, Julsrud PR (1989) Diagnostic selective balloon occlusion technique in pulmonic valve atresia and ventricular septal defect. Am J Cardiol 63: 1408–1409

    Article  PubMed  CAS  Google Scholar 

  45. Huhta JC, Piehler JM, Tajik AJ, Hagler DJ, Mair DD, Julsrud PR, Seward JB (1982) Two dimensional echocardiographic detection and measurement of the right pulmonary artery in pulmonary atresia-ventricular septal defect: angiographic and surgical correlation. Am J Cardiol 49: 1235–1240

    Article  PubMed  CAS  Google Scholar 

  46. Kaufman SL, Kan JS, Mitchell SE, Flaherty JT, White RIJ (1986) Embolization of systemic to pulmonary artery collaterals in the management of hemoptysis in pulmonary atresia. Am J Cardiol 58: 1130–1132

    Article  PubMed  CAS  Google Scholar 

  47. Kawata T, Hasegawa J, Yoshida Y, Kawachi K, Kita-mura S (1995) Usefulness of interlocking detachable coil for embolization of the major aorto-pulmonary collateral artery: a case report. Cathet Cardiovasc Diagn 34: 362–364

    Article  PubMed  CAS  Google Scholar 

  48. Kersting-Sommerhof BA, Sechtem UP, Higgins CB (1988) Evaluation of pulmonary blood supply by nuclear Magnetic resonance imaging in patients with pulmonary atresia. J Am Coll Cardiol 11: 166–171

    Article  Google Scholar 

  49. Kirklin JW, Bargeron LMJ, Pacifico AD (1977) The enlargement of small pulmonary arteries by preliminary palliative operations. Circulation 56: 612–617

    Article  PubMed  CAS  Google Scholar 

  50. Kirklin JW, Blackstone EH, Shimazaki Y, Maehara T, Pacifico AD, Kirklin JK, Bargeron LMJ (1988) Survival, functional status, and reoperations after repair of tetralogy of Fallot with pulmonary atresia. J Thorac Cardiovasc Surg 96: 102–116

    PubMed  CAS  Google Scholar 

  51. Kumar S, Scagliotti D, Fisher EA, del Nido P (1990) Surgical correction of pulmonary atresia with ventricular septal defect and no central pulmonary arteries. Am J Cardiol 65: 261–263

    Article  PubMed  CAS  Google Scholar 

  52. Liao PK, Edwards WD, Julsrud PR, Puga FJ, Danielson GK, Feldt RH (1985) Pulmonary blood supply in patients with pulmonary atresia and ventricular septal defect. J Am Coll Cardiol 6: 1343–1350

    Article  PubMed  CAS  Google Scholar 

  53. Luhmer I, Ziemer G (1993) Coarctation of the pulmonary artery in neonates. Prevalence, diagnosis, and surgical treatment. J Thorac Cardiovasc Surg 106: 43. 889–894

    PubMed  CAS  Google Scholar 

  54. Macartney FJ, Haworth SG (1978) The pulmonary blood supply in pulmonary atresia with ventricular septal defect. In: Godman MJ, Marquis RM (eds) Pediatric Cardiology, vol 2. Churchill Livingstone, Edinburgh, pp 314–329

    Google Scholar 

  55. Marelli AJ, Perloff JK, Child JS, Laks H (1994) Pulmonary atresia with ventricular septal defect in adults. Circulation 89: 243–251

    Article  PubMed  CAS  Google Scholar 

  56. McGoon DC, Baird DK, Davis GD (1975) Surgical stenosis or atresia. Circulation 52: 109–118

    Article  PubMed  CAS  Google Scholar 

  57. McGoon MD, Fulton RE, Davis GD, Ritter DG, Neill CA, White RIJ (1977) Systemic collateral and pulmoartery stenosis in patients with congenital pulmonary valve atresia and ventricular septal defect. Circulation 56: 473–479

    Article  PubMed  CAS  Google Scholar 

  58. McLeod KA, Blackburn ME, Gibbs JL (1994) Stenting of stenosed aortopulmonary collaterals: a new appalliation in pulmonary atresia with multi- 47. focal aortopulmonary blood supply. Br Heart J 71: 487–489

    Article  PubMed  CAS  Google Scholar 

  59. Miller WW, Nadas AS, Bernhard WF, Gross RE (1968) Congenital pulmonary atresia with ventricular defect. Review of the clinical course of fifty patients with assessment of the results of palliative surgery. Am J Cardiol 21: 673–680

    Google Scholar 

  60. Mocellin R, Sauer U, Schumacher G, Kellner M, Schober JG (1978) Effect of prostaglandin El on the hemodynamics in newborn infants with pulmonary atresia. Z Kardiol 67: 572–577

    PubMed  CAS  Google Scholar 

  61. Moller JH (1990) Incidence of cardiac malformations. In: Moller JH, Neal WA (eds) Fetal, neonatal and infant cardiac disease. Appleton and Lange, Norwalk, Ct, pp 361–369

    Google Scholar 

  62. Nakata S, Imai Y, Takanashi Y, Kurosawa H, Tezuka K, Nakazawa M, Ando M, Takao A (1984) A new method for the quantitative standardization of cross-sectional areas of the pulmonary arteries in congenital heart diseases with decreased pulmonary blood flow. J Thorac Cardiovasc Surg 88: 610–619

    PubMed  CAS  Google Scholar 

  63. Neutze JM, Starling MB, Elliott RB, Barratt Boyes. BG (1977) Palliation of cyanotic congenital heart disease in infancy with E-type prostaglandins. Circulation 55: 238–241

    Article  PubMed  CAS  Google Scholar 

  64. Olin CL, Ritter DG, McGoon DC, Wallace RB, Danielson GK (1976) Pulmonary atresia: surgical considerations and results in 103 patients undergoing definitive repair. Circulation 54:11135 —11140

    Google Scholar 

  65. Perry SB, Radtke W, Fellows KE, Keane JF, Lock JE (1989) Coil embolization to occlude aortopulmonary collateral vessels and shunts in patients with congen- 54. ital heart disease. J Am Coll Cardiol 13: 100–108

    Article  PubMed  CAS  Google Scholar 

  66. Puga FJ (1992) Surgical treatment of pulmonary atresia and ventricular septal defect. Prog Pediatr Cardiol 1: 37–49

    Article  Google Scholar 

  67. Puga FJ, Leoni FE, Julsrud PR, Mair DD (1989) Complete repair of pulmonary atresia, ventricular septal defect, and severe peripheral arborization abnormalities of the central pulmonary arteries. Experience with preliminary unifocalization procedures in 38 patients. J Thorac Cardiovasc Surg 98: 1018–1028

    PubMed  CAS  Google Scholar 

  68. Puga FJ, McGoon DC, Julsrud PR, Danielson GK, Mair DD (1983) Complete repair of pulmonary atresia with nonconfluent pulmonary arteries. Ann Thorac Surg 35: 36–44

    Article  PubMed  CAS  Google Scholar 

  69. Rabinovitch M, Herrera de Leon V, Castaneda AR, Reid L (1981) Growth and development of the pulmonary vascular bed in patients with tetralogy of Fallot with or without pulmonary atresia. Circulation 64: 1234–1249

    Article  PubMed  CAS  Google Scholar 

  70. Rees RS, Somerville J, Underwood SR, Wright J, Firmin DN, Klipstein RH, Longmore DB (1987) Magnetic resonance imaging of the pulmonary arteries and their systemic connections in pulmonary atresia: comparison with angiographie and surgical findings. Br Heart J 58: 621–626

    Article  PubMed  CAS  Google Scholar 

  71. Reichenspurner H, Netz H, Uberfuhr P, Wagner FM, Vetter HO, Reichart B (1994) Heart-lung transplantation in a patient with pulmonary atresia and ventricular septal defect. Ann Thorac Surg 57: 210–212

    Article  PubMed  CAS  Google Scholar 

  72. Rome JJ, Mayer JE, Castaneda AR, Lock JE (1993) Tetralogy of Fallot with pulmonary atresia. Rehabilitation of diminutive pulmonary arteries. Circulation 88: 1691–1698

    Google Scholar 

  73. Rothman A, Perry SB, Keane JF, Lock JE (1990) Early results and follow-up of balloon angioplasty for branch pulmonary artery stenoses. J Am Coll Cardiol 15: 1109–1117

    Article  PubMed  CAS  Google Scholar 

  74. Sawatari K, Imai Y, Kurosawa H, Isomatsu Y, Momma K (1989) Staged operation for pulmonary atresia and ventricular septal defect with major aortopulmonary collateral arteries. New technique for complete unifocalization. J Thorac Cardiovasc Surg 98: 738–750

    Google Scholar 

  75. Shimazaki Y, Maehara T, Blackstone EH, Kirklin JW, Bargeron LMJ (1988) The structure of the pulmonary circulation in tetralogy of Fallot with pulmonary atresia. A quantitative cineangiographic study. J Thorac Cardiovasc Surg 95: 1048–1058

    Google Scholar 

  76. Shimazaki Y, Mashiko I, Nakano S, Morimoto S, Ikawa S, Matsuda H, Kawashima Y (1991) Pulmonary artery morphology and hemodynamics in pulmonic valve atresia with ventricular septal defect before and after repair. Am J Cardiol 67: 744–748

    Article  PubMed  CAS  Google Scholar 

  77. Sieverding L, Breuer J, Jung WI, Schick F, Klose U, Fleiter T, Apitz J (1995) Möglichkeiten and Grenzen der Kernspintomographie in der Diagnostik von Herzfehlern. Monatsschr Kinderheilkd 143: 10641074

    Google Scholar 

  78. Smyllie JH, Sutherland GR, Keeton BR (1989) The value of Doppler color flow mapping in determining pulmonary blood supply in infants with pulmonary atresia with ventricular septal defect. J Am Coll Cardiol 14: 1759 —1765

    Google Scholar 

  79. Somerville J (1970) Management of pulmonary atresia. Br Heart J 32: 641–651

    Article  PubMed  CAS  Google Scholar 

  80. Spray TL, Mallory GB, Canter CB, Huddleston CB (1994) Pediatric lung transplantation. Indications, techniques, and early results. J Thorac Cardiovasc Surg 107: 990–999

    Google Scholar 

  81. Sullivan ID, Wren C, Stark J, de Leval MR, Macartney FJ, Deanfield JE (1988) Surgical unifocalization in pulmonary atresia and ventricular septal defect. A realistic goal? Circulation 78: 1115–11113

    Article  Google Scholar 

  82. Szarnicki R, Krebber HJ, Wack J (1981) Wire coil embolization of systemic-pulmonary artery collaterals following surgical correction of pulmonary atresia. J Thorac Cardiovasc Surg 81: 124–126

    PubMed  CAS  Google Scholar 

  83. Thiene G, Frescura C, Bini RM, Valente M, Gallucci V (1979) Histology of pulmonary arterial supply in pulmonary atresia with ventricular septal defect. Circulation 60: 1066–1074

    Article  PubMed  CAS  Google Scholar 

  84. Van Praagh R, Van Praagh S, Nebesar RA, Muster AJ, Sinha SN, Paul MH (1970) Tetralogy of Fallot: underdevelopment of the pulmonary infundibulum and its sequelae. Am J Cardiol 26: 25–33

    Article  PubMed  Google Scholar 

  85. Borromée L, Lecompte Y, Batisse A, et al. (1988) Anatomic repair of anomalies of ventriculoarterial connection associated with ventricular septal defect. II. Clinical results in 50 patients with pulmonary outflow tract obstruction. J Thorac Cardiovasc Surg 95: 96–102

    PubMed  Google Scholar 

  86. Kawashima Y, Fuyita T, Miyamoto T, Manabe H (1971) Intraventricular rerouting of blood for the correction of Taussig-Bing malformation. J Thorac Cardiovasc Surg 62: 825–829

    PubMed  CAS  Google Scholar 

  87. Kirklin JW, Barrat-Boyes BG (1993) Double outlet left ventricle. In: Kirklin JW, Barrat-Boyes BG (eds) Cardiac Surgery. Morphology, diagnostic criteria, natural history, techniques, results, and indications. Churchill Livingstone, New York Edinburgh London Melbourne Tokyo, pp 1501–1509

    Google Scholar 

  88. Kirklin JW, Barrat-Boyes BG (1993) Double outlet right ventricle. In: Kirklin JW, Barrat-Boyes BG (eds) Cardiac Surgery. Morphology, diagnostic criteria, natural history, techniques, results, and indications. Churchill Livingstone, New York Edinburgh London Melbourne Tokyo, pp 1469–1500

    Google Scholar 

  89. Lev M, Bharati S, Meng C, Liberthson RR, Paul MH, ldriss F (1972) A concept of double outlet right ventricle. J Thorac Cardiovasc Surg 64: 271–281

    PubMed  CAS  Google Scholar 

  90. Musumeci F, Shumway S, Lincoln C, Anderson RH (1988) Surgical treatment for double-outlet right ventricle at the Brompton hospital, 1973 —1986. J Thorac Cardiovasc Surg 96: 278–287

    PubMed  CAS  Google Scholar 

  91. Neufeld HN, Lucas RV, Lester RG, Adams P, Anderson RC, Edwards JE (1962) Origin of both great vessels from the right ventricle without pulmonary stenosis. Br Heart J 24: 393

    Article  PubMed  CAS  Google Scholar 

  92. Pacifico AD, Kirklin JK, Colvin EV, Bargeron LM (1986) Intraventricular tunnel repair for Taussig-Bing heart and related cardiac anomalies. Circulation 74 (Suppl I): 53–60

    Google Scholar 

  93. Patrick DL, McGoon DC (1968) An operation for double-outlet right ventricle with transposition of the great arteries. J Cardiovasc Surg 9: 537–542

    CAS  Google Scholar 

  94. Quaegebeur JM (1986) The arterial switch operation. Rationale, results and perspectives. [Thesis]. Leiden University, The Netherlands

    Google Scholar 

  95. Shen WK, Holmes DR, Porter CJ, McGoon DC, Ilstrup DM (1990) Sudden death after repair of double-outlet right ventricle. Circulation 81: 128–136

    Article  PubMed  CAS  Google Scholar 

  96. Taussig HB, Bing RJ (1949) Complete transposition of the aorta and a levoposition of the pulmonary artery: Clinical, physiological and pathological findings. Am Heart J 37: 551–559

    Google Scholar 

  97. Van Praagh R (1968) What is the Taussig-Bing-malformation? Circulation 38: 445–449

    Article  PubMed  Google Scholar 

  98. Van Praagh S, Davidoff A, Chin A, Shiel FS, Reynolds J, van Praagh R (1982) Double outlet right ventricle: anatomic types and developmental implications based on a study of 101 autopsied cases. Coeur 13: 389–439

    Google Scholar 

  99. Witham AC (1957) Double outlet right ventricle. A partial transposition complex. Am Heart J 53: 928–939

    Article  PubMed  CAS  Google Scholar 

  100. Anderson RH, Henry W, Becker AE (1991) Morphologic aspects of complete transposition. Cardiol Young 1:41— 53

    Google Scholar 

  101. Baillie M (1797) The morbid anatomy of the most important parts of the human body, 2nd ed. Johnson and Nicol, London, p 38

    Google Scholar 

  102. Bernuth von G, Däbritz S, Seghaye MC, et al. (1994) Beziehung zwischen kardialer Anatomie und Risiko der arteriellen Switch-Operation bei Neugeborenen mit kompletter Transposition der großen Arterien. Z Kardiol 83: 686–687

    Google Scholar 

  103. Beuren A (1966) Die Transpositionen der großen Gefäße. In: Opitz H, Schmid F (Hrsg) Handbuch der Kinderheilkunde, Bd VII. Springer, Berlin, Heidelberg, New York, 768–777

    Google Scholar 

  104. Björk VO, Bouckaert L (1954) Complete transposition of the aorta and the pulmonary artery. An experimental study of the surgical possibilities for its treatment. J Thorac Surg 28: 632–635

    Google Scholar 

  105. Blalock A, Hanlon CR (1950) The surgical treatment of complete transposition of the aorta and pulmonary artery. Surg Gynecol Obstet 90: 1–15

    PubMed  CAS  Google Scholar 

  106. Castaneda AR, Norwood WI, Jonas RA, Colan SD, Sanders SP, Lang P (1984) Transposition of the great arteries and intact ventricular septum: Anatomical repair in the neonate. Ann Thorac Surg 38: 438–443

    Google Scholar 

  107. Chang AC, Wernovsky G, Wessel DL, et al. (1992) Surgical management of late right ventricular failure after Mustard or Senning repair. Circulation 86 (Suppl II): 140–149

    Google Scholar 

  108. Colan SD, Trowitzsch E, Wernovsky G, Sholler GF, Sanders SP, Castaneda AR (1988) Myocardial performance after arterial switch operation for transposition of the great arteries with intact ventricular septum. Circulation 78: 132–141

    Article  PubMed  CAS  Google Scholar 

  109. Deanfield J, Camm J, Macartney FJ, et al. (1988) Arrhythmia and late mortality after Mustard and Senning operation for transposition of the great arteries. A eight-year prospective study. J Thorac Cardiovasc Surg 96: 569–576

    Google Scholar 

  110. Farre JR (1814) Pathological Researches. Essay 1: On malformations of the human heart. In: Longman, Hurst, Rees, Orme, Brown, London, p 28

    Google Scholar 

  111. Flinn CJ, Wolff GS, Dick M, et al. (1984) Cardiac rhythm after the Mustard operation for complete transposition of the great arteries. N Engl J Med 310: 1635–1638

    Article  PubMed  CAS  Google Scholar 

  112. Gewillig M, Cullen S, Mertens B, Lesaffre E, Dean-field J (1991) Risk factors for arrhythmia and death after Mustard operation for simple transposition of the great arteries. Circulation 84: 187–192

    Google Scholar 

  113. Gillette PC, Garson A (1990) Pediatric arrhythmias: Electrophysiology and pacing. WB Saunders, Philadelphia

    Google Scholar 

  114. Gittenberger-de Groot AC, Sauer U, Oppenheimer-Dekker A, Quaegebeur J (1983) Coronary arterial anatomy in transposition of the great arteries: A morphological study. Pediatr Cardiol 4 (Suppl 1): 15–24

    Google Scholar 

  115. Gittenberger-de Groot AC, Sauer U, Quaegebeur J (1986) Aortic intramural coronary artery in three hearts with transposition of the great arteries. J Thorac Cardiovasc Surg 91: 566–571

    Google Scholar 

  116. Izumo S, Nadal-Ginard B, Mandavi V (1988) Protooncogene induction and reprogramming of cardiac gene expression produced by pressure overload. Proc Natl Acad Sci USA 85: 339–344

    Article  PubMed  CAS  Google Scholar 

  117. Jonas RA, Giglia TM, Sanders SP, Wernovsky G, Nadal-Ginard B MJ, Castaneda AR (1989) Rapid, two-stage arterial switch for transposition of the great arteries and intact ventricular septum beyond the neonatal period. Circulation 80 (Suppl I): 203–208

    Google Scholar 

  118. Kirklin JW, Barrat-Boyes BG (1993) Complete transposition of the great arteries. In: Kirklin JW, BarratBoyes BG (eds) Cardiac Surgery. Morphology, diagnostic criteria, natural history, techniques, results, and indications. Churchill Livingstone, New York, Edinburgh, London, Melborne, Toyko, 1383–1467

    Google Scholar 

  119. Kramer HH, Majewski F, Trampisch HJ, Rammos S, Bourgeois M (1987) Malformation patterns in children with congenital heart disease. Am J Dis Childr 144: 789–795

    Google Scholar 

  120. Kramer HH, Trampisch Hi, Giese A, Rammos S (1990) Birth weight of children with congenital heart disease. Eur J Ped 149: 752–757

    Article  CAS  Google Scholar 

  121. Kramer HH, Rammos S, Krogmann O, Böker S, Ostermeyer J, Krian A (1991) Cardiac rhythm after Mustard repair and after anatomic correction of complete transposition of the great arteries. Int J Cardiol 32: 5–12

    Article  PubMed  CAS  Google Scholar 

  122. Kramer HH, Rammos S, Krian A, et al. (1992) Intermediate term clinical and hemodynamic results of the neonatal arterial switch operation for complete transposition of the great arteries. Int J Cardiol 36: 13–22

    Article  PubMed  CAS  Google Scholar 

  123. Kramer HH, Sommer M, Rammos S, Krogmann ON (1995) Evaluation of low dose prostaglandin El treatment for ductus dependent congenital heart disease. Eur J Ped 154: 700–707

    Article  CAS  Google Scholar 

  124. Lecompte Y, Zannini L, Hazan E, et al. (1981) Anatomic correction of transposition of the great arteries. New technique without use of a prosthetic conduit. J Thorac Cardiovasc Surg 82: 629–631

    Google Scholar 

  125. Liebman J, Cullum L, Belloc NB (1969) Natural history of transposition of the great arteries. Anatomy and birth and death characteristics. Circulation 40: 237–262

    Google Scholar 

  126. Mahony L, Turley K, Ebert P, Heymann MA (1982) Long-term results after atrial repair of transposition of the great arteries in early infancy. Circulation 66: 253–258

    Article  PubMed  CAS  Google Scholar 

  127. Mandell VS, Lock JE, Mayer JE (1990) The “laid back” aortogram: an improved angiographic view for demonstration of coronary arteries in transposition of the great arteries. Am J Cardiol 65: 1379–1383

    Article  PubMed  CAS  Google Scholar 

  128. Moene RJ, Oppenheimer-Dekker A, Wenink ACG, Bartelings MM, Gittenberger-de Groot AC (1985) Morphology of ventricular septal defect in complete transposition of the great arteries. Am J Cardiol 55: 1566–1570

    Article  PubMed  CAS  Google Scholar 

  129. Murphy JH, Barlai-Kovach MM, Mathews RA, et al. (1983) Rest and exercise right and left ventricular function late after the Mustard operation: assessment by radionuclide ventriculography. Am J Cardiol 51: 1520 —1526

    Google Scholar 

  130. Mustard WT (1964) Successful two-stage correction of transposition of the great vessels. 55: 469–472

    CAS  Google Scholar 

  131. Mustard WT, Chute AL, Keith JD, Sirek A, Rowe R, Vlad P (1954) A surgical approach to transposition of the great vessels with extracorporeal circuit. Surgery 36: 39–51

    Google Scholar 

  132. Neches WN, Park SC, Ettedgui JA (1990) Transposition of the great arteries. In: Garson Jr A BJ, McNamara DG (eds) The Science and Practice of Pediatric Cardiology. Lea und Febiger, Philadelphia/London, 1175–1212

    Google Scholar 

  133. Norwood WI, Dobell AR, Freed MD, Kirklin JW, Blackstone EH (1988) Intermediate results of the arterial switch repair. A 20-institution study. J Thorac Cardiovasc Surg 96: 854 —863

    Google Scholar 

  134. Park SC, Neches WH, Mathews RA, et al. (1983) Hemodynamic function after the Mustard operation for transposition of the great arteries. Am J Card 51: 1514–1519

    Article  PubMed  CAS  Google Scholar 

  135. Pasquini L, Parness I, Colan SD, Wernovsky G, Mayer JE, Sanders SP (1993) Diagnosis of intramural coronary artery in transposition of the great arteries using two-dimensional echocardiography. Circulation 88: 1136–1141

    Article  PubMed  CAS  Google Scholar 

  136. Quaegebeur JM (1986) The arterial switch operation. Rationale, results and perspectives. Thesis, Leiden University, The Netherlands

    Google Scholar 

  137. Quaegebeur JM, Rohmer J, Ottenkamp J, et al. (1986) The arterial switch operation. An eight-year experience. J Thorac Cardiovasc Surg 92: 361–384

    Google Scholar 

  138. Rashkind W, Miller W (1966) Creation of an atrial septal defect without thoracotomy: a palliative approach to complete transposition of the great arteries. JAMA 196: 991–992

    Article  PubMed  CAS  Google Scholar 

  139. Rastelli GC, Wallace RB, Ongley PA (1969) Complete repair of transposition of the great arteries with pulmonary stenosis. A review and report of a case corrected by using a new surgical technique. Circulation 39: 83–95

    Google Scholar 

  140. Senning A (1959) Surgical correction of transposition of the great vessels. Surgery 45: 966–980

    PubMed  CAS  Google Scholar 

  141. Serraf A, Lacour-Gayet F, Bruniaux J, et al. (1993) Anatomic correction of transposition of the great arteries in neonates. J Am Coll Cardiol 22: 193–200

    Article  PubMed  CAS  Google Scholar 

  142. Smith A, Arnold R, Wilkinson JL, Mamilton DI, McKay R, Anderson RH (1986) An anatomical study of the patterns of the coronary arteries and sinus nodal artery in complete transposition. Int J Cardiol 12: 295–304

    Article  PubMed  CAS  Google Scholar 

  143. Taussig HB, Bing RJ (1949) Complete transposition of the aorta and a levoposition of the pulmonary artery: Clinical, physiological and pathological findings. Am Heart J 37: 551–559

    Google Scholar 

  144. Tsuda E, Imakita M, Yagihara T, et al. (1992) Late death after arterial switch operation for transposition of the great arteries. Am Heart J 124: 1551–1557

    Article  PubMed  CAS  Google Scholar 

  145. Turina MI, Siebenmann R, Segesser von L, Schönbeck M, Senning A (1989) Late functional deterioration after atrial correction for transposition of the great arteries. Circulation 80: 162–167

    Google Scholar 

  146. Wernovsky G, Giglia TM, Jonas RA, Mone SM, Colan SD, Wessel DL (1992) Course in the intensive care unit after `preparatory’ pulmonary banding and aortopulmonary shunt placement for transposition of the great arteries with low left ventricular pressure. Circulation 86 (Suppl II): 133–139

    Google Scholar 

  147. Wernovsky G, Hougen TJ, Walsh EP, et al. (1988) Midterm results after the arterial switch operation for transposition of the great arteries with intact ventricular septum: clinical, hemodynamic, echocardiographic, and electrophysiologic data. Circulation 77: 1333–1344

    Article  PubMed  CAS  Google Scholar 

  148. Yacoub MH, Radley-Smith R, Hilton CJ (1976) Anatomical correction of complete transposition of the great arteries and ventricular septal defect in infancy. Br Med J 1: 1112–1114

    Article  PubMed  CAS  Google Scholar 

  149. Yacoub MH, Radley-Smith R, Maclaurin R (1977) Two-stage operation for anatomical correction of transposition of the great arteries with intact interventricular septum. Lancet 1: 1275–1278

    Article  PubMed  CAS  Google Scholar 

  150. Anderson RH, Arnold R, Wilkinson JL (1973) The conducting system in congenitally corrected transposition. Lancet 1: 1286–1288

    Article  PubMed  CAS  Google Scholar 

  151. Barth H (1994) Pädiatrische Echokardiographie. In: Leidig E, Grunert D (Hrsg) Pädiatrische Ultraschalldiagnostik und Duplexsonographie. Ecomed, Landsberg/Lech

    Google Scholar 

  152. Benson LN, Burns R, Schwaiger M, Schelbert HR, Lewis AB, Freedom RM, 011ey PM, McLaughlin P, Rowe RD (1986) Radionuclide angiographic evaluation of ventricular function in isolated congenitally corrected transposition of the great arteries. Am J Cardiol 58: 319–324

    Article  PubMed  CAS  Google Scholar 

  153. Beuren AJ, Stoermer J, Apitz J (1963) Die korrigierte Transposition der großen Gefäße bei situs solitus. Arch Kreislaufforsch 41: 228–252

    Article  PubMed  CAS  Google Scholar 

  154. Celermajer DS, Cullen S, Deanfield JE, Sullivan ID (1991) Congenitally corrected transposition and Ebstein’s anomaly of the systemic atrioventricular valve: association with aortic arch obstruction. J Am Coll Cardiol 18: 1056–1058

    Article  PubMed  CAS  Google Scholar 

  155. Daliento L, Corrado D, Buja G, John N, Nava A, Thiene G (1986) Rhythm and conduction disturbances in isolated, congenitally corrected transposition of the great arteries. Am J Cardiol 58: 314–318

    Article  PubMed  CAS  Google Scholar 

  156. Freedom RM, Dyck JD (1995) Congenitally corrected transposition of the great arteries. In: Emmanouilides GC, Allen HD, Riemenschneider TA, Gutgesell HP (eds) Moss and Adams heart disease in infants, children, and adolescents, fifth edition. Williams und Wilkins, Baltimore, pp 1225–1245

    Google Scholar 

  157. Fyler DC (1992) Nadas’ pediatric cardiology. Mosby Year Book, St. Louis, pp 701–708

    Google Scholar 

  158. Huhta JC, Danielson GK, Ritter DG, Ilstrup DM (1985) Survival in atrioventricular discordance. Pediatr Cardiol 6: 57–60

    Article  PubMed  CAS  Google Scholar 

  159. Meissner MD, Panidis IP, Eshaghpour E, Mintz GS, Ross J (1986) Corrected transposition of the great arteries: evaluation by two-dimensional and Doppler echocardiography. Am Heart J Ill: 599–601

    Google Scholar 

  160. Monckeberg JG (1913) Zur Entwicklungsgeschichte des Atrioventrikularsystems. Verh Dtsch Pathol Ges 16: 228–249

    Google Scholar 

  161. Presbitero P, Somerville J, Rabajoli F, Stone S, Conte MR (1995) Corrected transposition of the great arteries without associated defects in adult patients: clinical profile and follow up. Br Heart J 74: 57–59

    Article  PubMed  CAS  Google Scholar 

  162. Rokitansky C von (1875) Die Defekte der Scheidewände des Herzens. Path.-anatom. Abhandlung. Wilhelm Braumüller, Wien, S 83–86

    Google Scholar 

  163. Stümper O, Wright JGC, De Giovanni JV, Silove ED, Sethia B, Brawn WJ (1995) Combined atrial and arterial switch procedure for congenital corrected transposition with ventricular septal defect. Br Heart J 73: 479–482

    Article  PubMed  Google Scholar 

  164. Yagihara T, Kishimoto H, Isobe F, Yamamoto F, Nishigaki K, Matsuki O, Kemura H, Kamiya T, Kawashima Y (1994) Double switch operation in cardiac anomalies with atrioventricular and ventriculoarterial discordance. J Thorac Cardiovasc Surg 107: 351–358

    PubMed  CAS  Google Scholar 

  165. Anderson RC, Obata W, Lillehei CW (1957) Truncus arteriosus: clinical study of 14 cases. Circulation 16: 586–598

    Article  PubMed  CAS  Google Scholar 

  166. Apitz J (1966) Truncus arteriosus communis persistens und Pseudotruncus arteriosus. In: Opitz H, Schmid F (Hrsg) Handbuch der Kinderheilkunde, Bd VII. Springer, Heidelberg, pp 569–579

    Google Scholar 

  167. Apitz J, Beuren AJ (1963) Angeborene Herzfehler im ersten Lebensjahr. Arch Kreisl Forsch 42: 264–276

    Article  CAS  Google Scholar 

  168. Apitz J, Stoermer J (1967) Über die Lebensaussichten von Säuglingen mit kongenitalen Angiokardiopathien. Mschr Kinderheilk 115: 95 —102

    Google Scholar 

  169. Collett RW, Edwards JE (1949) Persistent truncus arteriosus: a classification according to anatomic types. Surg Clin N Amer 29: 1245 —1270

    Google Scholar 

  170. Doerr R (1943) Über Mißbildungen des menschlichen Herzens mit besonderer Berücksichtigung von Bulbus und Truncus. Virchows Arch path Anat 310: 304

    Google Scholar 

  171. Ebert PA, Turley K, Stanger P, Hoffmann JIE, Heymann MA, Rudolph AM (1984) Surgical treatment of truncus arteriosus in the first 6 months of life. Ann Surg 200: 451–456

    Article  PubMed  CAS  Google Scholar 

  172. Fyler DC (1992) Nadas’ Pediatric Cardiology. Hanley und Belfus, Philadelphia, pp 675–681

    Google Scholar 

  173. Goerttler K (1958) Normale und pathologische Entwicklung des menschlichen Herzens. Thieme, Stuttgart, pp 22–41

    Google Scholar 

  174. Hofbeck M (1994) Truncus arteriosus communis. In: Schmaltz AA, Singer H (Hrsg) Herzoperierte Kinder und Jugendliche. Wiss Verlagsges, Stuttgart, pp 281–293

    Google Scholar 

  175. Keith JD, Rowe RD, Vlad P (1958) Heart Disease in infancy and childhood. Macmillan Comp, New York, pp 521–534

    Google Scholar 

  176. McGoon DC, Rastelli GC, Ongley PA (1968) An operation for the correction of truncus arteriosus. JAMA 205: 59–73

    Article  Google Scholar 

  177. Sieverding L, Klose U, Apitz J (1990) Morphological diagnosis of congenital and acquired heart disease by Magnetic Resonance Imaging. Pediatr Radiol 20: 311–319

    Article  PubMed  CAS  Google Scholar 

  178. Taussig HB (1960) Congenital malformations of the heart, 2nd ed, Vol II. Commonwealth Fund, Cambridge, USA, pp 275–316

    Google Scholar 

  179. Van Praagh R, Van Praagh S (1965) The anatomy of common aorticopulmonary trunk (truncus arteriosus communis) and its embryologic implications. Amer J Cardiol 16: 406–425

    Article  PubMed  Google Scholar 

  180. Williams RL, Sommerville RJ (1990) Truncus arteriosus. In: Garsson A, Bricker JT, McNamara DG (eds) The science and practice of Pediatric Cardiology. Lea und Febiger, Philadelphia, pp 1127–1133

    Google Scholar 

  181. Ziemer G, Borst HG (1991) Truncus arteriosus. In: Borst HG, Klinner W, Oelert H (Hrsg) Kirschnersche allgemeine und spezielle Operationslehre, Bd VI, Teil 2. Springer, Heidelberg, pp 251–260

    Google Scholar 

  182. Zuckermann R (1965) Herzauskultation, 2. Aufl. Thieme, Leipzig, pp 199–200, 378

    Google Scholar 

  183. De Leval MR, Killner P, Gewillig M, Bull C (1988) Total cavopulmonary connection. A logical alternative to atriopulmonary connection for complex Fontan operations. J Thorac Cardiovasc Surg 96: 682–695

    Google Scholar 

  184. De Vivie ER, Rupprath G (1986) Long term results after Fontan Procedure and its modifications. J Thorac Cardiovasc Surg 91: 690–696

    PubMed  Google Scholar 

  185. Fontan F, Kirklin JW, Fernandez G, Costa F, Naftel DC, Tritto F, Blackstone EH (1990) Outcome after a “perfect” Fontan operation. Circulation 81: 1520–1535

    Article  PubMed  CAS  Google Scholar 

  186. Grant GP, Mansell AL, Garofano RP, Hayes CH, Bowman Jr FO, Gersony WW (1988) Cardiorespiratory response to exercise after the Fontan Procedure for tricuspid atresia. Pediatr Res 24: 1–5

    Article  PubMed  CAS  Google Scholar 

  187. Holmes WF (1824) Case of malformation of the heart. Trans Med CHIR Soc Edinburgh 1: 252

    Google Scholar 

  188. Kotthoff S (1991) Langzeitbeobachtungen nach der Fontan-Operation. Z Herz-Thorax-Gefäßchir 5 (Suppl I): 19–22

    Google Scholar 

  189. Mair DD, Hagler DJ, Puga FJ, Schaff HV, Danielson GK (1990) Fontan Operation in 176 patients with tricuspid atresia. Circulation 82 (Suppl IV): 164–169

    Article  Google Scholar 

  190. Mair DD, Hagler DJ, Julsrud PR, Puga FJ, Schaff HV, Danielson GK (1991) Early and late results of the modified Fontan procedure for double-inlet left ventricle: the Mayo Clinic experience. JACC 18: 1727–1732

    PubMed  CAS  Google Scholar 

  191. Vlad P (1978) Tricuspid. atresia. In: Keith JD, Rowe RD, Vlad P (eds) Heart disease in infancy and childhood, 3rd ed. Macmillan Co., New York, pp 518–541

    Google Scholar 

  192. Alboliras ET, Julsrud PR, Danielson GK, Puga FJ, Schaff HV, McGoon DC, Hagler DJ, Edwards WD, Driscoll D (1987) Definite operation for pulmonary atresia with intact ventricular septum. J Thorac Cardiovasc Surg 93: 454–464

    PubMed  CAS  Google Scholar 

  193. Anderson RH, Macartney FJ, Shinebourne EA, Tynan M (1987) Pediatric Cardiology. Churchill Livingstone, Edinburgh London Melbourne New York, pp 711–720

    Google Scholar 

  194. De Leval M, Bull C, Stark J, Anderson RH, Taylor JFN, Maccartney FJ (1982) Pulmonary atresia and intact ventricular septum: Surgical management based on a revised classification. Circulation 66: 272–280

    Google Scholar 

  195. Hunter J (1784) Three cases of malformation in the heart. Med Obsery Enquir 6: 291

    Google Scholar 

  196. Milliken JC, Laks H, Hellenbrand BG, Chin A, Williams RG (1985) Early and late results in the treatment of patients with pulmonary atresia and intact ventricular septum. Circulation 72 (Suppl II): 61–69

    Article  Google Scholar 

  197. Peacock TB (1869) Malformation of the heart: Atresia of the orifice of the pulmonary artery. Trans Pathol Soc Lond 20: 61

    Google Scholar 

  198. Schmaltz AA, Singer H (1994) Herzoperierte Kinder und Jugendliche. Wissenschaftliche Verlagsgesellschaft mbH, Stuttgart, S 142–148

    Google Scholar 

  199. Schmaltz AA, Hinkeldey K, Hoffmeister HE, Apitz J (1985) Prognose der Kinder mit kongenitaler Trikuspidal-und Pulmonalatresie in den Jahren 1967–83 im Vergleich zum natürlichen Verlauf. Monatsschr Kinderheilk 133: 743 —748

    Google Scholar 

  200. Akagi T, Benson LN, Gilday DL, Ash J, Green M, Williams WG, Freedom RM (1993) Influence of ventricular morphology on diastolic filling performance in double inlet ventricle after the Fontan procedure. J Am Coll Cardiol 22: 1948–1952

    Article  PubMed  CAS  Google Scholar 

  201. Allgood NL, Alejos J, Drinkwater DC, Laks H, Williams RG (1994) Effectiveness of the bidirectional Glenn shunt procedure for volume unloading in the single ventricle patient. Am J Cardiol 74: 834–836

    Article  PubMed  CAS  Google Scholar 

  202. Anderson RH, Macartney FJ, Tynan M, Becker AE, Freedom RM, Godman MJ, Hunter S, Quero-Jiminez M, Rigby ML, Shinebourne EA, Sutherland G, Small-horn JG, Soto B, Thiene G, Wilkinson JL, Wilcox BR, Zuberbuhler JR (1983) Univentricular atrioventricular connection: the single ventricle trap unsprung. Pediatr Cardiol 4: 273–280

    Article  PubMed  CAS  Google Scholar 

  203. Anderson RH, Becker AE, Tynan M, Macartney FJ, Rigby ML, Wilkinson JL (1984) The univentricular atrioventricular connection. Getting to the root of a thorny problem. Am J Cardiol 54: 822–828

    Google Scholar 

  204. Cheung HC, Lincoln CL, Anderson RH, Ho SY, Shine-bourne EA, Pallides S, Rigby ML (1990) Options for surgical repair in hearts with univentricular atrioventricular connection and subaortic stenosis. J Thorac Cardiovasc Surg 100: 672–681

    PubMed  CAS  Google Scholar 

  205. Cromme-Dijkhuis AH, Hess J, Hählen K, Henkens CMA, Bink-Bölkens MTE, Eygelaar AA, Bos E (1993) Specific sequelae after Fontan operation at mid-and long-term follow-up. J Thorac Cardiovasc Surg 106: 1126–1132

    PubMed  CAS  Google Scholar 

  206. Feldt RH, Mair D, Danielson GK, Wallace RB, McGoon DC (1981) Current status of the septation procedure for univentricular heart. J Thorac Cardiovasc Surg 82: 93–97

    PubMed  CAS  Google Scholar 

  207. Freedom RM, Culham JAG, Moes CAF (1984) Single ventricle. In: Freedom RM, Culham JAG, Moes CAF (eds) Angiocardiography of congenital heart disease. Macmillan Publishing Company, New York, pp 593–628

    Google Scholar 

  208. Freedom RM, Benson LN, Smallhorn JF, Williams WG, Trusler GA, Rowe RD (1986) Subaortic steno-sis, the univentricular heart, and banding of the pulmonary artery: an analysis of the courses of 43 patients with univentricular heart palliated by pulmonary artery banding. Circulation 73: 758–764

    Article  PubMed  CAS  Google Scholar 

  209. Hagler DJ, Edwards WD (1995) Univentricular atrioventricular connection. In: Emmanouilides GC, Allen HD, Riemenschneider TA, Gutgesell HP (eds) Moss and Adams heart disease in infants, children and adolescents, fifth edition. William und Wilkins, Baltimore, pp 1278–1306

    Google Scholar 

  210. Holmes AF (1824) Case of malformation of the heart. Trans Med-Chir Soc Edinb 1:252–259 (zit. bei [141)

    Google Scholar 

  211. Mair DD, Hagler DJ, Julsrud PR, Puga Fi, Schaff HN, Danielson GK (1991) Early and late results of the modified Fontan procedure for double inlet left ventricle: The Mayo Clinic experience. J Am Coll Cardiol 18: 1727–1732

    Google Scholar 

  212. Moodie DS, Ritter DG, Tajik AJ, O’Fallon WM (1984) Long-term follow-up in the unoperated univentricular heart. Am J Cardiol 53: 1124–1128

    Article  PubMed  CAS  Google Scholar 

  213. Schumacher G, Bühlmeyer K (1989) Double inlet ventricle. In: Schumacher G, Bühlmeyer K (Hrsg) Diagnostik angeborener Herzfehler, 2. Aufl. Perimed, Erlangen, S 632–650

    Google Scholar 

  214. Stefanelli G, Kirklin JW, Naftel DC, Blackstone EH, Pacifico AD, Kirklin JK, Soto B, Bargeron LM (1984) Early and intermediate-term (10-year) results of surgery for univentricular atrioventricular connection (“single ventricle”). Am J Cardiol 54: 811–821

    Article  PubMed  CAS  Google Scholar 

  215. Thies WR, Soto B, Diethelm E, Bargeron LM, Pacifico AD (1985) Angiographie anatomy of hearts with one ventricular chamber: The true single ventricle. Am J Cardiol 55: 1363–1366

    Google Scholar 

  216. Van Praagh R, Ongley PA, Swan HJC (1964) Anatomic types of single or common ventricle in man: morphologic and geometric aspects of sixty necropsied cases. Am J Cardiol 13: 367–386

    Article  Google Scholar 

  217. Van Praagh R, David I, Van Praagh S (1982) What is a ventricle? The single ventricle trap. Pediatr Cardiol 2: 79–84

    Article  PubMed  Google Scholar 

  218. Wilson J (1798) A description of a very unusual formation of the human heart. Phil Trans B 18: 332 (zit. bei [141)

    Google Scholar 

  219. Freedom RM, Culham JAG, Moes CAF (1984) Mitral atresia. In: Freedom RM, Culham JAG, Moes CAF (eds) Angiocardiography of congenital heart disease. Macmillan Publishing Company, New York, pp 303–314

    Google Scholar 

  220. Hofbeck M, Singer H, Taylor JFN (1987) Mitralatresie mit normaler Aortenklappe und Pulmonalatresie. Herz 12: 413–418

    PubMed  CAS  Google Scholar 

  221. Puga F, Chiavarelli M, Hagler DJ (1987) Modifications of the Fontan operation applicable to patients with left atrioventricular valve atresia or single atrioventricular valve. Circulation 76 (Suppl III): 53–60

    Google Scholar 

  222. Shinpo H, Van Praagh S, Parness I, Sanders S, Molthan M, Castaneda A (1992) Mitral atresia with a large left ventricle and an underdeveloped or absent right ventricular sinus: Clinical profile, anatomic data and surgical considerations. J Am Coll Cardiol 19: 1561–1576

    Google Scholar 

  223. Shore D, Jones O, Rigby ML, Anderson RH, Lincoln C (1982) Atresia of left atrioventricular connection. Surgical considerations. Br Heart J 47: 35–40

    Google Scholar 

  224. Thiene G, Daliento L, Frescura C, De Tommasi M, Macartney F, Anderson RH (1981) Atresia of left atrioventricular orifice. Anatomical investigation in 62 cases. Br Heart J 45: 393–401

    Article  PubMed  CAS  Google Scholar 

  225. Apitz J (1989) Hypoplastisches Linksherzsyndrom. In: Bachmann et al. (Hrsg) Pädiatrie in Praxis und Klinik, 2. Aufl, Bd 1. Fischer, Thieme, Stuttgart, S 790–793

    Google Scholar 

  226. Apitz J, Stoermer J (1967) Über die Lebensaussichten von Säuglingen mit kongenitalen Angiokardiopathien. Monatsschr Kinderheilkd 115: 95–102

    PubMed  CAS  Google Scholar 

  227. Apitz J, Stoermer J (1967) Klinik und Pathologie der Aortenatresie. Monatsschr Kinderheilkd 115: 365371

    Google Scholar 

  228. Burk GK (1989) Pathologie und Klinik des hypoplastischen Linksherzsyndroms. Inaugural-Dissertation Tübingen

    Google Scholar 

  229. Canton J (1849) Congenital obliteration of origin of the Aorta. Trans path Soc, London 2: 38

    Google Scholar 

  230. Dilg J (1883) Ein Beitrag zur Kenntnis seltener Herzanomalien im Anschluß an einen Fall von angeborener linksseitiger Conusstenose. Arch Pathol Anat 91: 193

    Article  Google Scholar 

  231. Eyler DC (1992) Nadas’ Pediatric Cardiology, Hanley und Belfus, Philadelphia, pp 623–634

    Google Scholar 

  232. Gaissmaier U, Apitz J (1972) Klinik und Pathologie des hypoplastischen Linksherzsyndroms. Zeitschr Kreislfforschg 61: 1003–1018

    CAS  Google Scholar 

  233. Murdison KA, Baffa JM, Farrell PE jr, Chang AC, Barber G, Norwood WI, Murphy JD (1990) Hypoplastic left-heart Syndrome. Circulation 82 (Suppl IV): 199

    Google Scholar 

  234. Noonan JA, Nadas AS (1958) The hypoplastic left heart Syndrome. Pediat Clin North Amer 5: 1029–1056

    CAS  Google Scholar 

  235. Norwood WI, Lang P, Hansen DD (1983) Physiologic repair of aortic atresia — hypoplastic left heart Syndrome. New Engl J Med 308: 23–26

    Article  PubMed  CAS  Google Scholar 

  236. Pigott JD, Norwood WI (1989) Hypoplastic left heart Syndrome. In: Cowgill LD (ed) Cardiac Surgery. Hanley und Belfus, Philadelphia, pp 217–224

    Google Scholar 

  237. Roberts WC, Perry LW, Chandra RS, Myers GE, Shapiro SR, Scott LP (1976) Aortic valve atresia: A new classification based on necropsy study of 73 cases. Amer J Cardiol 37: 753–756

    Article  PubMed  CAS  Google Scholar 

  238. Sinha SN, Rusnack SL, Sommers HM, Cole RB, Muster AJ, Paul MH (1968) Hypoplastic left ventricle Syndrome. Amer J Cardiol 21: 166–173

    Article  PubMed  CAS  Google Scholar 

  239. Schmaltz AA, Singer H (1994) Herzoperierte Kinder und Jugendliche. Wiss Verlagsges, Stuttgart, S 193–196

    Google Scholar 

  240. Schumacher G, Bühlmeyer K (1980) Diagnostik angeborener Herzfehler, Bd II. Perimed, Erlangen, S 69–88

    Google Scholar 

  241. Castaneda AR, Jonas RA, Mayer JE, Hanley FL (1994) Cardiac surgery of the neonate and infant: Anomalies of the pulmonary veins. Saunders, Philadelphia London Toronto, pp 157–166

    Google Scholar 

  242. Darling RC, Rothney WB, Craig JM (1957) Total pulmonary venous drainage into the right side of the heart. Lab Invest 6: 44–49

    PubMed  Google Scholar 

  243. Deslile G, Ando M, Caler AL, Zuberbuhler JR, Rodenmacher S, Alday LE, Mangini O, van Praagh S, van Praagh R (1976) Total anomalous pulmonary venous connection: Report of 93 autopsied cases with emphasis on diagnostic and surgical considerations. Am Heart J 91: 99–113

    Article  Google Scholar 

  244. Driscoll DJ, Hesslein PS, Mullins CE (1982) Congenital stenosis of individual pulmonary veins: Clinical spectrum and unsuccessful treatment by transvenous balloon dilation. Am J Cardiol 49: 1767–1772

    Google Scholar 

  245. Huhta JC, Gutgesell HP, Nihill MR (1985) Cross-sectional echocardiographic diagnosis of total anomalous pulmonary venous connection. Br Heart J 53: 525–534

    Article  PubMed  CAS  Google Scholar 

  246. Klein MD, Shaheen KW, Whitlesey GC (1990) Extracorporeal membrane oxygenation for the circulation support of children after repair of congenital heart disease. J Thorac Cardiovasc Surg 100: 489–494

    Google Scholar 

  247. Krabill KA, Lucas RV jr (1995) Abnormal pulmonary venous connections. In: Emmanouilides GC, Riemenschneider TA, Allen HD, Gutgesell HP (eds) Moss and Adams Heart disease in infants, children, and adolescents, including the fetus and young adult. Fifth ed. Williams und Wilkins, Baltimore Philadelphia Hongkong, pp 838–874

    Google Scholar 

  248. Lima CO, Valdes-Cruz LM, Allen HD (1983) Prognostic value of left ventricular size measured by echocardiography in infants with total anomalous pulmonary venous drainage. Am J Cardiol 51: 1155–1159

    Article  Google Scholar 

  249. McMullan MH, Fyke FE III (1992) Total anomalous pulmonary venous connection: Surgical correction in a 66-year-old man. Ann Thorac Surg 53: 520–522

    Article  PubMed  CAS  Google Scholar 

  250. Musewe NN, Smallhorn JF, Freedom RM (1991) Anomalies of pulmonary venous connections including cor triatriatum and stenosis of individual pulmonary veins. In: Freedom RM, Benson LN, Smallhorn JF (eds) Neonatal heart disease. Springer, London Berlin Heidelberg New York, pp 309–331

    Google Scholar 

  251. Oppermann HC, Wille L, Ulmer HE (1982) Der Neugeborenen-Thorax. Röntgenologische Diagnose and Differentialdiagnose. Springer, Berlin Heidelberg New York, pp 146–150

    Google Scholar 

  252. Pacifico AD, Mandke NV, McGrath LB (1972) Repair of congenital pulmonary venous drainage to the coronary sinus. J Thorac Cardiovasc Surg 64: 132

    Google Scholar 

  253. Paster SB, Swensson RE, Yabec SM (1977) Total anomalous pulmonary venous connection. Pediatr Radiol 6: 132–135

    Article  PubMed  CAS  Google Scholar 

  254. Rodriguez-Collado J, Attie F, Zabal C, Troyo P, 01vera S, Vazquez J, Gutiérrez B, Vargas-Barron J (1992) Total anomalous pulmonary venous connection in adults: Long-term follow-up. J Thorac Cardiovasc Surg 103: 877–880

    Google Scholar 

  255. Rose V, Izukawa T, Moës CAF (1975) Syndromes of asplenia and polysplenia: A review of cardiac and non cardiac malformations in 60 cases with special reference to diagnosis and prognosis. Br Heart J 37: 840–852

    Article  PubMed  CAS  Google Scholar 

  256. Sano G, Brawn WJ, Mee RBB (1989) Total anomalous pulmonary venous drainage. J Thorac Cardiovasc Surg 97: 886

    PubMed  CAS  Google Scholar 

  257. Smallhorn JF, Sutherland GR, Tomagini G, Hunter S, Anderson RH, Macartney FJ (1981) Assessment of total anomalous pulmonary venous connection by two-dimensional echocardiography. Br Heart J 46: 613–623

    Article  PubMed  CAS  Google Scholar 

  258. Smallhorn JF, Panperio H, Benson L, Freedom RM, Rowe RD (1985) Pulsed doppler assessment of pulmonary vein obstruction. Am Heart J 110: 483–486

    Article  PubMed  CAS  Google Scholar 

  259. Saxena A, Fong LV, Lamb RK, Monro JL, Shore DF, Keeton BM (1991) Cardiac arrhythmias after surgical correction of total anomalous pulmonary venous connection: Late follow-up. Pediatr Cardiol 12: 89–91

    Google Scholar 

  260. Turley K, Tucher WY, Ullyot DJ, Ebert PA (1980) Total anomalous pulmonary venous connection in infancy: Influence of age and type of lesion. Am J Cardiol 45: 92–97

    Google Scholar 

  261. van der Velde M, Parness IA, Colan SD (1991) Two dimensional echocardiography in the pre-and postoperative management of total anomalous pulmonary venous connection. J Am Coll Cardiol 18: 1746

    Article  PubMed  Google Scholar 

  262. Apitz J, Stoermer J (1967) Über die Lebensaussichten von Säuglingen mit kongenitalen Angiokardiopathien. Mschr Kinderheilkd 115: 95–102

    CAS  Google Scholar 

  263. Becker AE, Anderson RH (1981) Pathology of congenital heart disease. Butterworths, London, pp 47–52

    Google Scholar 

  264. Beuren AJ (1966) Die angiokardiographische Darstellung kongenitaler Herzfehler. de Gruyter, Berlin, S 95–96, 305–307

    Google Scholar 

  265. Edwards JE (1960) Congenital malformations of the Thoracic Veins. In: Gould SE (ed) Pathology of the Heart 2“d ed. CC Thomas Publ, Springfield, Ill, pp 481–483

    Google Scholar 

  266. Edwards JE, DuShane JW (1950) Thoracic venous anomalies. Arch Path 49: 517–537

    Google Scholar 

  267. Fischer DR, Zuberbuhler JR (1987) Anomalous systemic venous return. In: Anderson RH, Macartney FJ, Shinebourne EA, Tynan M (eds) Paediatric Cardiology, vol I. Churchill Livingstone, Edinburgh, pp 497 —508

    Google Scholar 

  268. Fowler NO (1980) Cardiac diagnosis and treatment, 3rd ed. Harper and Row Publ, Cambridge, pp 489491, 945

    Google Scholar 

  269. Goerttler K (1958) Normale und pathologische Entwicklung des menschlichen Herzens. Thieme, Stuttgart, S 96–97

    Google Scholar 

  270. Goerttler K (1963) Die Mißbildungen des Herzens und der großen Gefäße. In: Bargmann W, Doerr W (Hrsg) Das Herz des Menschen, Bd I. Thieme, Stuttgart, S 510–513

    Google Scholar 

  271. Huhta JC (1990) Anomalies of systemic venous return. In: Garson A, Bricker JT, McNamara DG (eds) The science and practice of pediatric cardiology, vol II. Lea und Febiger, Philadelphia, pp 1462–1470

    Google Scholar 

  272. Perloff JK (1978) The clinical recognition of congenital heart disease, 2“ ed. WB Saunders, Philadelphia, pp 715–722

    Google Scholar 

  273. Raghib G, Ruttenberg HD, Anderson RC, Amplatz K, Adams P, Edwards JE (1965) Termination of the left superior vena cava in left atrium, atrial septal defect and absence of coronary sinus. Circulation 31: 906–918

    Article  PubMed  CAS  Google Scholar 

  274. Castaneda AR, Jonas RA, Mayer JE jr, Hanley FL (1994) Cardiac surgery of the neonate and infant: Ebstein’s anomaly. Saunders, Philadelphia London Toronto, pp 273–280

    Google Scholar 

  275. Celermajer DS, Cullen S, Sullivan ID, Spiegelhalter DS, Wyse RKH, Deanfield JE (1992) Outcome in neonates with Ebstein’s anomaly. J Am Coll Cardiol 19: 1041–1046

    Article  PubMed  CAS  Google Scholar 

  276. Celermajer DS, Bull C, Till JA, Cullen S, Vassillikos VP, Sullivan ID, Allan L, Nihoyamopoulos P, Somerville J, Deanfield JE (1994) Ebstein’s Anomaly: Presentation and outcome from fetus to adult. J Am Coll Cardiol 23: 170–176

    Google Scholar 

  277. Danielson GK, Driscoll DJ, Mair DD, Wornes CA, Oliver WC jr (1992) Operative treatment of Ebstein’s Anomaly. J Thorac Cardiovasc Surg 104: 1195–1202

    PubMed  CAS  Google Scholar 

  278. Ebstein W (1866) Über einen sehr seltenen Fall von Insuffizienz der Valvula tricuspidalis bedingt durch eine angeborene hochgradige Mißbildung derselben. Arch Anat Physiol 238–254

    Google Scholar 

  279. Fram DB, Missri J, Therrien ML, Chaiola S (1991) Assessment of Ebstein’s anomaly and its surgical repair using transesophageal two-dimensional echocardiography and doppler color flow mapping. Echocardiography 8: 367–371

    Article  Google Scholar 

  280. Freedom RM, Benson LN (1991) Ebstein’s malformation of the tricuspid valve. In: Freedom RM, Benson LN, Smallhorn JF (eds) Neonatal Heart Disease. Springer, London Berlin Heidelberg New York, pp 471–483

    Google Scholar 

  281. Gentles TL, Calder L, Clarkson PM, Neutze JM (1992) Predictors of long-term survival with Ebstein’s anomaly of the tricuspid valve. Am J Cardiol 69: 377–381

    Article  PubMed  CAS  Google Scholar 

  282. Long WA, Willis PW (1984) Maternal lithium and neonatal Ebstein’s. Am J Perinatol 1: 182–184

    Article  PubMed  CAS  Google Scholar 

  283. Pressley JC, Wharton M, Lang ASL, Lowe JE, Gallangher JJ, Prystowsky EN (1992). Effect of Ebstein’s anomaly on short-and long-term outcome of surgically treated patients with Wolff-Parkinson-White Syndrome. Circulation 86: 1147–1155

    Article  PubMed  CAS  Google Scholar 

  284. Roberson DA, Silverman NH (1989) Ebstein’s anomaly: Echocardiographic and clinical features in the fetus and neonate. J Am Coll Cardiol 14: 1300–1307

    Google Scholar 

  285. Saxena A, Fang LV, Tristan M, Ackery DM, Keaton BR (1991) Late noninvasive evaluation of cardiac performance in mildly symptomatic older patients with Ebstein’s anomaly of the tricuspid valve: role of radionuclide imaging. J Am Coll Cardiol 17: 182–186

    Article  PubMed  CAS  Google Scholar 

  286. Seward JB, Tajik AJ, Feist DJ, Smith HC (1979) Ebstein’s anomaly in an 85-year-old man. Mayo Clinic Proc 54: 193–196

    CAS  Google Scholar 

  287. Sharland GK, Chita SK, Allan LD (1991) Tricuspid valve dysplasia or displacement in intrauterine life. J Am Coll Cardiol 17: 944–949

    Article  PubMed  CAS  Google Scholar 

  288. Waickman LA, Skorton DJ, Varner MW, Ehmke DA, Goplerud CP (1984) Ebstein’s anomaly and pregnancy. Am J Cardiol 53: 357–358

    Article  PubMed  CAS  Google Scholar 

  289. Watson H (1974) Natural history of Epstein’s anomaly of tricuspid valve in childhood and adolescence. An international co-operative study of 505 cases. Br Heart J 36: 417–427

    Article  PubMed  CAS  Google Scholar 

  290. Zalzstein E, Karen G, Einarson T, Freedom M (1990) A case-control study on the association between first trimester exposure to lithium and Ebstein’s anomaly. Am J Cardiol 65: 817–818

    Article  PubMed  CAS  Google Scholar 

  291. Zuberbuhler JR, Anderson RH (1988) Ebstein’s malformation of the tricuspid valve: morphology and natural history. In: Anderson RH et al. (eds): Perspectives in pediatric cardiology. Vol 1. Futura, Mount Kisco, New York, pp 99–112

    Google Scholar 

  292. Adatia I, Haworth SG (1993) Circulating endothelin in children with congenital heart diseases. Br Heart J 69: 233–236

    Article  PubMed  CAS  Google Scholar 

  293. Breuer J, Georgoraki A, Sieverding L, Baden W, Apitz J (1996) Increased serotonin turnover in children with pulmonary hypertension secondary to congenital heart disease. Ped Cardiol 17: 214–219

    Article  CAS  Google Scholar 

  294. Celermajer DS, Cullen S, Deanfield JE (1993) Impairment of endothelium-dependent pulmonary artery relaxation in children with congenital heart disease and abnormal pulmonary hemodynamics. Circulation 87: 440–446

    Article  PubMed  CAS  Google Scholar 

  295. Celermajer DS, Dollery C, Burch M, Deanfield JE (1994) Role of endothelium in the maintenance of low pulmonary vascular tone in normal children. Circulation 89: 2041–2044

    Article  PubMed  CAS  Google Scholar 

  296. Christman BW, McPherson CD, Newman JH, King GA, Bernard GR, Groves BM, Loyd JE (1992) An imbalance between the excretion of thromboxane and prostacyclin metabolites in pulmonary hypertension. N Engl J Med 327: 70–75

    Article  PubMed  CAS  Google Scholar 

  297. Dinh-Xuan AT, Higenbottam TW, Clelland C, PepkeZaba J, Cremona G, Wallwork J (1989) Impairment of pulmonary endothelium-dependent relaxation in patients with Eisenmenger’s syndrome. Br J Pharmacol 99: 9–10

    Article  Google Scholar 

  298. Furchgott RF, Zawadzki JV (1980) The obligatory role of the endothelial cells in the relaxation of arterial smooth muscle by acetylcholine. Nature 288: 373–376

    Article  PubMed  CAS  Google Scholar 

  299. Fuse S, Kamiya T (1994) Plasma thromboxane B2 concentration in pulmonary hypertension associated with congenital heart disease. Circulation 90: 2952–2955

    Article  PubMed  CAS  Google Scholar 

  300. Gildein HP, Wildberg A, Mocellin R (1995) Vergleichende Untersuchungen der Hämodynamik unter Prostazyklin and Nifedipin bei Patienten mit Eisenmenger-Syndrom. Z Kardiol 84: 55–63

    PubMed  CAS  Google Scholar 

  301. Hall SM, Haworth SG (1992) Onset and evolution of pulmonary vascular disease in young children: Abnormal postnatal remodelling studied in lung biopsies. J Pathol 166: 183–193

    Google Scholar 

  302. Haworth SG (1987) Pulmonary vasculature. In: Anderson RH, Shinebourne EA, Macartney FJ, Tynan M (Hrsg) Paediatric Cardiology. Churchill Livingstone, Edinburgh, pp 123–157

    Google Scholar 

  303. Heath D, Edwards J (1958) The pathology of hypertensive pulmonary vascular disease. Circulation 18: 533–547

    Article  PubMed  CAS  Google Scholar 

  304. Hentrich F (1994) Pulmonale Hypertonie and obstruktive Lungengefäßerkrankung. In: Schmatz AA, Singer H (Hrsg) Herzoperierte Kinder and Jugendliche. Wiss Verlagsgesellschaft, Stuttgart, S 65–74

    Google Scholar 

  305. Hoffmeister HE, Apitz J, Fischbach H, Hoffmeister HM (1988) Hämodynamik and Histologie der Lungengefäße bei 191 Patienten mit atrio-ventrikulärem Kanal. Klin Pädiatr 200: 96–101

    Article  PubMed  CAS  Google Scholar 

  306. Ignarro LJ, Byrns RE, Buga GM, Wood KS (1987) Endothelium-derived relaxing factor from pulmonary artery and vein possesses pharmacologic and chemical properties identical to those of nitric oxide radical. Circulation Res 61: 866–879

    Article  PubMed  CAS  Google Scholar 

  307. Ilkiw RL, Miller-Hance WC, Nihill MR (1990) The pulmonary circulation. In: Garson A, Bricker JT, McNamara DG (eds) The science and practice of pediatric cardiology. Lea und Febiger, Philadelphia, pp 361–385

    Google Scholar 

  308. Krovetz LJ, McLughlin TG, Mitchell MB (1967) Hemodynamic findings in normal children. Pediatr Res 1: 122–130

    Article  PubMed  CAS  Google Scholar 

  309. Lock JE, Einzig S, Moller JH (1982) Hemodynamic responses to exercise. Am J Cardiol 41: 1278–1284

    Article  Google Scholar 

  310. New York Heart Association, Criteria Committee (1979) Nomenclature and criteria for diagnosis of diseases of the heart and great vessels. Little, Brown and Co, Boston, pp 276–278

    Google Scholar 

  311. Noonan JA (1990) Cor pulmonale. In: Chernick V, Kendig EL (eds) Kendig’s Disorders of the respiratory tract in children. Saunders, Philadelphia, pp 683–692

    Google Scholar 

  312. Palmer RMJ, Ferrige AG, Moncada S (1987) Nitric oxide release accounts for the biological activity of endothelium-derived relaxing factor. Nature 327: 524–526

    Article  PubMed  CAS  Google Scholar 

  313. Paridon SM (1990) Consequences of chronic hypoxemia and pulmonary vascular disease. In: Garson A, Bricker JT, McNamara DG (eds) The science and practice of pediatric cardiology. Lea und Febiger, Philadelphia, pp 1996–2006

    Google Scholar 

  314. Rabinovitch M, Keane JH, Fellows KE (1981) Quantitative analysis of the pulmonary wedge angiogram in congenital heart disease: correlation with hemodynamic data and morphometric findings in lung biopsy tissue. Circulation 63: 152–164

    Article  PubMed  CAS  Google Scholar 

  315. Riediger G, Grävinghoff LM, Höhne KH, Keck EW (1988) Digital cine angiographic evaluation of pulmonary blood flow velocity in ventricular septal defect. Cardiovasc Intervent Radiol 11: 1–4

    Article  PubMed  CAS  Google Scholar 

  316. Roberts JD, Lang P, Bigatello LM, Vlahakes GJ, Zapol WM (1993) Inhaled nitric oxide in congenital heart diseae. Circulation 87: 447 —453

    Google Scholar 

  317. Vanhoutte PM (1993) Other endothelium-derived vasoactive factors. Circulation 87 (Suppl V): V9 - V17

    CAS  Google Scholar 

  318. Vincent JA, Ross RD, Kassab J, Hsu JM, Pinsky WW (1993) Relation of elevated plasma endothelin in congenital heart disease to increased pulmonary blood flow. Am J Cardiol 71: 1204–1207

    Article  PubMed  CAS  Google Scholar 

  319. Wagenvoort CA, Wagenvoort N (1977) Pathology of pulmonary hypertension. Wiley, New York, p 48

    Google Scholar 

  320. Wimmer M, Schlemmer M, Ebner F (1988) Hemodynamic effects of nifedipine and oxygen in children with pulmonary hypertension. Cardiovasc Drug Ther 2: 661–668

    Article  CAS  Google Scholar 

  321. Yoshibayashi M, Nishioka K, Nakao K, Saito Y, Matsumura M, Ueda T, Temma S, Shirakami G, Imura H, Mikawa H (1991) Plasma endothelin concentrations in patients with pulmonary hypertension associated with congenital heart disease. Circulation 84: 2280–2285

    Article  PubMed  CAS  Google Scholar 

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  1. J. Apitz
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  1. Lehrstuhl für Kinderkardiologie, Neuklinikum der Universität, Hoppe-Seyler-Str. 3, 72076, Tübingen, Deutschland

    Jürgen Apitz (Ärztlicher Direktor der Abteilung Kinderheilkunde II mit Poliklinik) (Ärztlicher Direktor der Abteilung Kinderheilkunde II mit Poliklinik)

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Apitz, J. et al. (1998). (Komplexe) Angeborene Herzfehler mit überwiegendem Rechts-Links-Shunt. In: Apitz, J. (eds) Pädiatrische Kardiologie. Steinkopff, Heidelberg. https://doi.org/10.1007/978-3-642-53754-7_8

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