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Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy

From Desmosome to Disease

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Clinical Cardiogenetics

Abstract

Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy (ARVD/C) is a disease characterized by progressive fibrofatty replacement of primarily the right ventricle (RV). 1–3

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  1. Department of Cardiology, University Medical Centre, Utrecht, The Netherlands

    Moniek G. P. J. Cox

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  1. Moniek G. P. J. Cox
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  2. Richard N. W. Hauer
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Correspondence to Moniek G. P. J. Cox .

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  1. University Medical Centre Utrecht, Heidelberglaan 100, 3584 CX, Utrecht, 3508 GA, Netherlands

    H.F. Baars

  2. University Medical Centre Utrecht, Heidelberglaan 100, 3584 CX, Utrecht, 3508 GA, Netherlands

    P.A.F.M. Doevendans

  3. University Medical Centre Utrecht, Heidelberglaan 100, 3584 CX, Utrecht, 3508 GA, Netherlands

    J.J. van der Smagt

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Cox, M.G.P.J., Hauer, R.N.W. (2011). Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy. In: Baars, H., Doevendans, P., van der Smagt, J. (eds) Clinical Cardiogenetics. Springer, London. https://doi.org/10.1007/978-1-84996-471-5_5

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