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Catecholaminergic Polymorphic Ventricular Tachycardia

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Clinical Cardiogenetics

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Abstract

Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a highly malignant inherited arrhythmia syndrome, characterized by bidirectional or polymorphic ventricular tachycardia (VT) and ventricular fibrillation (VF) during physical or emotional stress in structurally normal hearts. This disease is illustrative of the progress that has been made in the field of cardiogenetics in the last decennia.

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Author information

Authors and Affiliations

  1. Department of Cardiology, Heart Failure Research Centre, Academic Medical Centre, Amsterdam, The Netherlands

    Christian van der Werf

Authors
  1. Christian van der Werf
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  2. Arthur A. M. Wilde
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Corresponding author

Correspondence to Christian van der Werf .

Editor information

Editors and Affiliations

  1. University Medical Centre Utrecht, Heidelberglaan 100, 3584 CX, Utrecht, 3508 GA, Netherlands

    H.F. Baars

  2. University Medical Centre Utrecht, Heidelberglaan 100, 3584 CX, Utrecht, 3508 GA, Netherlands

    P.A.F.M. Doevendans

  3. University Medical Centre Utrecht, Heidelberglaan 100, 3584 CX, Utrecht, 3508 GA, Netherlands

    J.J. van der Smagt

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van der Werf, C., Wilde, A.A.M. (2011). Catecholaminergic Polymorphic Ventricular Tachycardia. In: Baars, H., Doevendans, P., van der Smagt, J. (eds) Clinical Cardiogenetics. Springer, London. https://doi.org/10.1007/978-1-84996-471-5_12

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  • DOI: https://doi.org/10.1007/978-1-84996-471-5_12

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  • Online ISBN: 978-1-84996-471-5

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