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Journal of Autism and Developmental Disorders

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12-05-2017 | Brief Report

Brief Report: Contrasting Profiles of Everyday Executive Functioning in Smith–Magenis Syndrome and Down Syndrome

Auteurs: Lucy Wilde, Chris Oliver

Gepubliceerd in: Journal of Autism and Developmental Disorders | Uitgave 8/2017

Abstract

Everyday executive function (EF) was examined in Smith–Magenis syndrome (SMS), associated with high risk of behaviour disorder, and Down syndrome (DS), associated with relatively low risk of behaviour disorder. Caregivers of 13 children with SMS and 17 with DS rated everyday EF using the Behavioral Rating Inventory of Executive Functioning-Preschool. Greater everyday EF deficits relative to adaptive ability were evident in SMS than in DS. The SMS profile of everyday EF abilities was relatively uniform; in DS emotional control strengths and working memory weaknesses were evident. Findings implicate broad everyday EF difficulties in SMS compared to DS, corresponding with increased rates of behaviour disorder in SMS. Findings further suggest that everyday EF profiles may, in part, be syndrome related.

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This difference was also significant in Mann–Whitney analysis, U = 17.5, p < .001.

This difference was also significant in a Wilcoxon analysis Z = −2.54, p = .011.

These differences were also significant in a Wilcoxon analysis; Inhibit Z = −3.43, p = .001, Plan/Organize Z = −3.32, p = .001 and Working Memory Z = −3.62, p < .001 but not Shift Z = −2.38, p = .017.

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Titel: Brief Report: Contrasting Profiles of Everyday Executive Functioning in Smith–Magenis Syndrome and Down Syndrome
Auteurs: Lucy Wilde
Chris Oliver
Publicatiedatum: 12-05-2017
Uitgeverij: Springer US
Gepubliceerd in: Journal of Autism and Developmental Disorders / Uitgave 8/2017
Print ISSN: 0162-3257
Elektronisch ISSN: 1573-3432
DOI: https://doi.org/10.1007/s10803-017-3140-2

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