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18-08-2016 | Heart Beat | Uitgave 11/2016 Open Access

Netherlands Heart Journal 11/2016

Anomalous left coronary artery arising from the pulmonary artery in an adult women

Netherlands Heart Journal > Uitgave 11/2016
M. C. de Kleijn, S. H. H. Kuijpers, F. J. Meijboom
A 47-year-old female was seen with chest pain and dyspnoea. She was diagnosed with an anomalous origin of the left coronary artery arising from the pulmonary artery or ALCAPA. This was previously known as the Bland-White-Garland syndrome. This congenital heart disease is a rare diagnosis in adults. Symptoms are angina, heart failure, ventricular arrhythmias, syncope or sudden death. Most patients are discovered in the first months of their lives, but patients can survive into adulthood because of an extremely large right coronary artery and an efficient network of collaterals [ 1, 2]. Specific echocardiographic changes are a large ostium of the right coronary artery and intercoronary septal collaterals (Fig.  1a; [ 3]). A 64-slice CT scan or MRI can be helpful in the diagnosis of ALCAPA (Fig.  1b). The treatment is re-implantation of the anomalous coronary into the aorta directly or with the help of a pulmonary flap. Treatment is necessary to prevent sudden cardiac death. [ 4, 5].
Open Access This article is distributed under the terms of the Creative Commons Attribution 4.0 International License ( http://​creativecommons.​org/​licenses/​by/​4.​0/​), which permits unrestricted use, distribution, and reproduction in any medium, provided you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons license, and indicate if changes were made.

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Netherlands Heart Journal

Het Netherlands Heart Journal wordt uitgegeven in samenwerking met de Nederlandse Vereniging voor Cardiologie en de Nederlandse Hartstichting. Het tijdschrift is Engelstalig en wordt gratis beschikbaa ...

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