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Sophie Van Malderen is double first author.
A 20-year-old sportive male presented with palpitations. Two-dimensional transthoracic echocardiography showed a severely dilated right atrium and a dislocated lateral tricuspid valve towards the right ventricular apex (Fig. 1a) with grade II tricuspid regurgitation (Fig. 1b). The 3D delayed enhancement study by cardiac MRI confirmed that the inferolateral leaflet of the tricuspid valve was 2.7 cm displaced apically, and septal and anterior leaflets were normally implanted (Fig. 2a and b). No intracardiac shunting was found. We conclude that this represents a not previously described form of Ebstein’s anomaly in which the septal and anterior leaflets were not displaced.
In a typical Ebstein's anomaly, the septal and inferior leaflets of the tricuspid valve are displaced apically  and the anterior leaflet is excessively large, and abnormally attached to the right ventricular free wall .
To the best of our knowledge, this is the first reported case of an isolated displacement of the inferior tricuspid valve leaflet in Ebstein’s anomaly.
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Diagnosis and Management of Adult Congenital Heart Disease. Sondergaard L and Cullen S. p283–287 Ebstein Anomaly.
Zuberbuhler JR, Allwork SP, Anderson RH. The spectrum of Ebstein's anomaly of the tricuspid valve. J Thorac Cardiovasc Surg. 1979;77(2):202–11. PubMed
- An unique case of “Atypical Ebstein’s Anomaly” with only isolated displacement of the inferior tricuspid leaflet
S. Van Malderen
D. E. Verdries
J. De Mey
G. Van Camp
- Bohn Stafleu van Loghum