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01-08-2014 | Imaging in Cardiology | Uitgave 7-8/2014 Open Access

Netherlands Heart Journal 7-8/2014

An unique case of “Atypical Ebstein’s Anomaly” with only isolated displacement of the inferior tricuspid leaflet

Netherlands Heart Journal > Uitgave 7-8/2014
K. Tanaka, S. Van Malderen, D. E. Verdries, J. De Mey, G. Van Camp
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Sophie Van Malderen is double first author.
A 20-year-old sportive male presented with palpitations. Two-dimensional transthoracic echocardiography showed a severely dilated right atrium and a dislocated lateral tricuspid valve towards the right ventricular apex (Fig. 1a) with grade II tricuspid regurgitation (Fig. 1b). The 3D delayed enhancement study by cardiac MRI confirmed that the inferolateral leaflet of the tricuspid valve was 2.7 cm displaced apically, and septal and anterior leaflets were normally implanted (Fig. 2a and b). No intracardiac shunting was found. We conclude that this represents a not previously described form of Ebstein’s anomaly in which the septal and anterior leaflets were not displaced.
In a typical Ebstein's anomaly, the septal and inferior leaflets of the tricuspid valve are displaced apically [1] and the anterior leaflet is excessively large, and abnormally attached to the right ventricular free wall [2].
To the best of our knowledge, this is the first reported case of an isolated displacement of the inferior tricuspid valve leaflet in Ebstein’s anomaly.
Open Access This article is distributed under the terms of the Creative Commons Attribution License which permits any use, distribution, and reproduction in any medium, provided the original author(s) and the source are credited.

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Netherlands Heart Journal

Het Netherlands Heart Journal wordt uitgegeven in samenwerking met de Nederlandse Vereniging voor Cardiologie en de Nederlandse Hartstichting. Het tijdschrift is Engelstalig en wordt gratis beschikbaa ...

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